Kremer Hovinga, Johanna Anna

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Journal Article

Vrotniakaite-Bajerciene, Kristina; Tritschler, Tobias; Jalowiec, Katarzyna Aleksandra; Broughton, Helen; Schmidli, Fabienne; Schneider, Jenny Sarah; Haynes, Alan; Rovo, Alicia; Kremer Hovinga, Johanna Anna; Aujesky, Drahomir; Angelillo, Anne (2023). Adherence to thrombophilia testing guidelines and its influence on anticoagulation therapy: A single-center cross-sectional study. Thrombosis research, 223, pp. 87-94. Elsevier 10.1016/j.thromres.2022.12.001

Tarasco, Erika; von Krogh, Anne Sophie; Hrdlickova, Radomira; Braschler, Thomas R; Iwaniec, Teresa; Knöbl, Paul N; Hamada, Eriko; Pikovsky, Oleg; Farese, Stefan; Gutwein, Odit; Kessler, Petr; Schultz, Nina H; von Auer, Charis; Windyga, Jerzy; Friedman, Kenneth; Hrachovinova, Ingrid; George, James N; Matsumoto, Masanori; Schneppenheim, Reinhard; Lämmle, Bernhard; ... (2022). Hereditary thrombotic thrombocytopenic purpura and COVID-19: Impacts of vaccination and infection in this rare disease. Research and practice in thrombosis and haemostasis, 6(7), e12814. Wiley 10.1002/rth2.12814

Vrotniakaite-Bajerciene, Kristina; Tritschler, Tobias; Jalowiec, Katarzyna Aleksandra; Broughton, Helen; Brodard, Justine; Porret, Naomi; Haynes, Alan; Rovo, Alicia; Kremer Hovinga, Johanna Anna; Aujesky, Drahomir; Angelillo-Scherrer, Anne (2022). Thrombophilia Impact on Treatment Decisions, Subsequent Venous or Arterial Thrombosis and Pregnancy-Related Morbidity: A Retrospective Single-Center Cohort Study. Journal of clinical medicine, 11(14), p. 4188. MDPI 10.3390/jcm11144188

Krzywicka, Katarzyna; van de Munckhof, Anita; Zimmerman, Julian; Bode, Felix J; Frisullo, Giovanni; Karapanayiotides, Theodoros; Pötzsch, Bernd; Sanchez Van Kammen, Mayte; Heldner, Mirjam R.; Arnold, Marcel; Kremer Hovinga, Johanna Anna; Ferro, Jose M; Aguiar de Sousa, Diana; Coutinho, Jonathan M (2022). Cerebral venous thrombosis due to vaccine-induced immune thrombotic thrombocytopenia after a second ChAdOx1 nCoV-19 dose. Blood, 139(17), pp. 2720-2724. American Society of Hematology 10.1182/blood.2021015329

Mertins, Tamara; Nilius, Henning; Boss, Robin; Knuchel, Matthias; Signorell, Andri; Huber, Carola A; Blozik, Eva; Kremer Hovinga, Johanna Anna; Bachmann, Lucas M; Nagler, Michael (2022). Secondary prevention of venous thromboembolism: Predictors and outcomes of guideline adherence in a long-term prospective cohort study. Frontiers in cardiovascular medicine, 9, p. 963528. Frontiers 10.3389/fcvm.2022.963528

Nilius, Henning; Mertins, Tamara; Boss, Robin; Knuchel, Matthias; Blozik, Eva; Kremer Hovinga, Johanna Anna; Eichinger, Sabine; Nagler, Michael (2021). Long-Term Survival After Venous Thromboembolism: A Prospective Cohort Study. Frontiers in cardiovascular medicine, 8(749342), p. 749342. Frontiers 10.3389/fcvm.2021.749342

Esteves Pereira, Michael; Bocksrucker, Christoph; Kremer Hovinga, Johanna Anna; Mueller, Martin; Daskalakis, Michael; Mansouri Taleghani, Behrouz; Nagler, Michael (2021). Immunoadsorption for the Treatment of Acquired Hemophilia: New Observational Data, Systematic Review, and Meta-Analysis. Transfusion medicine reviews, 35(2), pp. 125-134. Elsevier 10.1016/j.tmrv.2021.01.001

Jalowiec, Katarzyna A.; Andres, Martin; Mansouri Taleghani, Behrouz; Musa, Albulena; Dickenmann, Martina; Angelillo-Scherrer, Anne; Rovó, Alicia; Kremer Hovinga, Johanna Anna (2020). Acquired hemophilia A and plasma cell neoplasms: a case report and review of the literature. Journal of medical case reports, 14(1), p. 206. BioMed Central 10.1186/s13256-020-02505-7

Schneider, Conrad; Stutz-Grunder, E; Lüer, Sonja; Keller, Heinz Peter; Kremer Hovinga, Johanna Anna; Ammann, R A; Karow, Axel (2019). Fulminant Essential Thrombocythemia Associated with Acquired Von Willebrand Syndrome and Bleeding Episodes in a 14-year-old Girl. Hämostaseologie, 39(4), pp. 404-408. Thieme 10.1055/s-0039-1679929

Schmid, Manuela; Spichiger, Elisabeth; Kremer Hovinga, Johanna Anna (2019). Aufbau einer interprofessionellen Betreuung für Patientinnen/Patienten mit angeborenen Hämostasestörungen (In Press). Pflegewissenschaft H P S Media 10.3936/1588

Kremer Hovinga, Johanna Anna; Heeb, Silvan Rolf; Skowronska, Magdalena; Schaller Tschan, Monica Maria (2018). Pathophysiology of thrombotic thrombocytopenic purpura and hemolytic uremic syndrome. Journal of thrombosis and haemostasis, 16(4), pp. 618-629. Wiley-Blackwell 10.1111/jth.13956

Prince Eladnani, Raja; Bologna, Luca; Manetti, Mirko; Melchiorre, Daniela; Rosa, Irene; Dewarrat, Natacha; Suardi, Silvia; Amini, Poorya; Fernández, José A; Burnier, Laurent; Quarroz, Claudia; Reina Caro, Maria Desiré; Matsumura, Yasuhiro; Kremer Hovinga, Johanna Anna; Griffin, John H; Simon, Hans-Uwe; Ibba-Manneschi, Lidia; Saller, François; Calzavarini, Sara and Angelillo, Anne (2018). Targeting anticoagulant protein S to improve hemostasis in hemophilia. Blood, 131(12), pp. 1360-1371. American Society of Hematology 10.1182/blood-2017-09-800326

Scully, Marie; Knöbl, Paul; Kentouche, Karim; Rice, Lawrence; Windyga, Jerzy; Schneppenheim, Reinhard; Kremer Hovinga, Johanna Anna; Kajiwara, Michiko; Fujimura, Yoshihiro; Maggiore, Caterina; Doralt, Jennifer; Hibbard, Christopher; Martell, Leah; Ewenstein, Bruce (2017). A recombinant human ADAMTS-13: first-in-human study evaluating pharmacokinetics, safety and tolerability in cTTP patients. Blood, 130(19), pp. 2055-2063. American Society of Hematology 10.1182/blood-2017-06-788026

Peyvandi, F; Scully, M; Kremer Hovinga, Johanna Anna; Knöbl, P; Cataland, S; De Beuf, K; Callewaert, F; De Winter, H; Zeldin, R K (2017). Caplacizumab reduces the frequency of major thromboembolic events, exacerbations, and death in patients with acquired thrombotic thrombocytopenic purpura. Journal of thrombosis and haemostasis, 15(7), pp. 1448-1452. Wiley-Blackwell 10.1111/jth.13716

Page, Evaren E; Kremer Hovinga, Johanna Anna; Terrell, Deirdra R; Vesely, Sara K; George, James N (2017). Thrombotic thrombocytopenic purpura: diagnostic criteria, clinical features, and long-term outcomes from 1995 through 2015. Blood advances, 1(10), pp. 590-600. American Society of Hematology 10.1182/bloodadvances.2017005124

Kremer Hovinga, Johanna Anna; Coppo, Paul; Lämmle, Bernhard; Moake, Joel L; Miyata, Toshiyuki; Vanhoorelbeke, Karen (2017). Thrombotic thrombocytopenic purpura. Nature reviews. Disease Primers, 3(17020), p. 17020. Nature Publishing Group 10.1038/nrdp.2017.20

Kremer Hovinga, Johanna Anna; Scharf, Rüdiger E (2017). Progress in Haemostasis. From individual patients to pathophysiological insights. Hämostaseologie, 37(1), pp. 9-11. Schattauer

Scully, M; Cataland, S; Coppo, P; de la Rubia, J; Friedman, K D; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; Matsumoto, M; Pavenski, K; Sadler, E; Sarode, R; Wu, H (2017). Consensus on the standardization of terminology in thrombotic thrombocytopenic purpura and related thrombotic microangiopathies. Journal of thrombosis and haemostasis, 15(2), pp. 312-322. Wiley-Blackwell 10.1111/jth.13571

Kölm, Robert; Schaller Tschan, Monica; Roumenina, Lubka T; Niemiec, Iga; Kremer Hovinga, Johanna Anna; Khanicheh, Elham; Kaufmann, Beat A; Hopfer, Helmut; Trendelenburg, Marten (2016). Von Willebrand Factor Interacts with Surface-Bound C1q and Induces Platelet Rolling. Journal of immunology, 197(9), pp. 3669-3679. American Association of Immunologists 10.4049/jimmunol.1501876

Page, Evaren E; Kremer Hovinga, Johanna Anna; Terrell, Deirdra R; Vesely, Sara K; George, James N (2016). Clinical importance of ADAMTS13 activity during remission in patients with acquired thrombotic thrombocytopenic purpura. Blood, 128(17), pp. 2175-2178. American Society of Hematology 10.1182/blood-2016-06-724161

Nagler, Michael; Kremer Hovinga, Johanna Anna; Alberio, Lorenzo; Peter-Salonen, Kristiina; von Tengg-Kobligk, Hendrik; Lottaz, Daniel; Neerman-Arbez, Marguerite; Lämmle, Bernhard (2016). Thromboembolism in patients with congenital afibrinogenaemia. Long-term observational data and systematic review. Thrombosis and haemostasis, 116(4), pp. 722-732. Schattauer 10.1160/TH16-02-0082

Pavenski, Katerina; Cataland, Spero; Kremer Hovinga, Johanna Anna; Thomas, Mari; Vanhoorelbeke, Karen (2016). Thrombotic thrombocytopenic pupura (TTP) dinner symposium proceedings. Expert review of hematology, 9(8), pp. 733-735. Expert Reviews 10.1080/17474086.2016.1198895

Pedrazzini, Giovanni; Biasco, Luigi; Sulzer, Irmela; Anesini, Adriana; Moccetti, Tiziano; Kremer Hovinga, Johanna Anna; Alberio, Lorenzo (2016). Acquired intracoronary ADAMTS13 deficiency and VWF retention at sites of critical coronary stenosis in patients with STEMI. Blood, 127(23), pp. 2934-2936. American Society of Hematology 10.1182/blood-2015-12-688010

Page, Evaren E; Kremer Hovinga, Johanna Anna; Terrell, Deirdra R; Vesely, Sara K; George, James N (2016). Rituximab reduces risk for relapse in patients with thrombotic thrombocytopenic purpura. Blood, 127(24), pp. 3092-3094. American Society of Hematology 10.1182/blood-2016-03-703827

Fan, Xinping; Kremer Hovinga, Johanna Anna; Shirotani-Ikejima, Hiroko; Eura, Yuka; Hirai, Hidenori; Honda, Shigenori; Kokame, Koichi; Mansouri Taleghani, Magnus; von Krogh, Anne-Sophie; Yoshida, Yoko; Fujimura, Yoshihiro; Lämmle, Bernhard; Miyata, Toshiyuki (2016). Genetic variations in complement factors in patients with congenital thrombotic thrombocytopenic purpura with renal insufficiency. International journal of hematology, 103(3), pp. 283-291. Springer 10.1007/s12185-015-1933-7

Peyvandi, Flora; Scully, Marie; Kremer Hovinga, Johanna Anna; Cataland, Spero; Knöbl, Paul; Wu, Haifeng; Artoni, Andrea; Westwood, John-Paul; Mansouri Taleghani, Magnus; Jilma, Bernd; Callewaert, Filip; Ulrichts, Hans; Duby, Christian; Tersago, Dominique (2016). Caplacizumab for Acquired Thrombotic Thrombocytopenic Purpura. New England journal of medicine NEJM, 374(6), pp. 511-522. Massachusetts Medical Society MMS 10.1056/NEJMoa1505533

von Krogh, A S; Quist-Paulsen, P; Waage, A; Langseth, Ø O; Thorstensen, K; Brudevold, R; Tjønnfjord, G E; Largiadèr, Carlo Rodolfo; Lämmle, Bernhard; Kremer Hovinga, Johanna Anna (2016). High prevalence of hereditary thrombotic thrombocytopenic purpura in Central Norway: from clinical observation to evidence. Journal of thrombosis and haemostasis, 14(1), pp. 73-82. Wiley-Blackwell 10.1111/jth.13186

Kremer Hovinga, Johanna Anna (2016). 111 années après Alexis Nikolaïevitch Romanov, guérison de l’hémophilie B sévère en perspective. Schweizerisches Medizin-Forum SMF / Swiss medical forum / Forum médical suisse FMS, 16(1), pp. 9-11. EMH Editores Medicorum Helveticorum

von Krogh, Anne-Sophie; Kremer Hovinga, Johanna Anna; Romundstad, Pål R; Roten, Linda T; Lämmle, Bernhard; Waage, Anders; Quist-Paulsen, Petter (2015). ADAMTS13 gene variants and function in women with preeclampsia: a population- based nested case- control study from the HUNT Study. Thrombosis research, 136(2), pp. 282-288. Elsevier 10.1016/j.thromres.2015.06.022

Hubbard, A R; Heath, A B; Kremer Hovinga, Johanna Anna (2015). Establishment of the WHO 1st International Standard ADAMTS13, plasma (12/252): communication from the SSC of the ISTH. Journal of thrombosis and haemostasis, 13(6), pp. 1151-1153. Wiley-Blackwell 10.1111/jth.12881

Arni, Delphine; Gumy-Pause, Fabienne; Ansari, Marc; Kremer Hovinga, Johanna Anna; McLin, Valérie A (2015). Successful liver transplantation in a child with acute-on-chronic liver failure and acquired thrombotic thrombocytopenic purpura. Liver transplantation, 21(5), pp. 704-706. Wiley 10.1002/lt.24096

von Auer, Charis; von Krogh, Anne-Sophie; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard (2015). Current insights into thrombotic microangiopathies: Thrombotic thrombocytopenic purpura and pregnancy. Thrombosis research, 135(Suppl1), S30-S33. Elsevier 10.1016/S0049-3848(15)50437-4

Raval, Jay S.; Padmanabhan, Anand; Kremer Hovinga, Johanna Anna; Kiss, Joseph E. (2015). Development of a clinically significant ADAMTS13 inhibitor in a patient with hereditary thrombotic thrombocytopenic purpura. American journal of hematology, 90(1), E22-E22. Wiley-Liss 10.1002/ajh.23851

Jiménez-Alcázar, M; Napirei, M; Panda, R; Köhler, E C; Kremer Hovinga, Johanna Anna; Mannherz, H G; Peine, S; Renné, T; Lämmle, Bernhard; Fuchs, T A (2015). Impaired DNase1-mediated degradation of neutrophil extracellular traps is associated with acute thrombotic microangiopathies. Journal of thrombosis and haemostasis, 13(5), pp. 732-742. Wiley-Blackwell 10.1111/jth.12796

Edgar, Contessa E; Terrell, Deirdra R; Vesely, Sara K; Wren, Jonathan D; Dozmorov, Igor M; Niewold, Timothy B; Brown, Michael; Zhou, Fang; Frank, Mark Barton; Merrill, Joan T; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; James, Judith A; George, James N; Farris, A Darise (2015). Ribosomal and Immune Transcripts Associate with Relapse in Acquired ADAMTS13-Deficient Thrombotic Thrombocytopenic Purpura. PLoS ONE, 10(2), e0117614. Public Library of Science 10.1371/journal.pone.0117614

Schaller Tschan, Monica; Vogel, Monique; Kentouche, Karim; Lämmle, Bernhard; Kremer Hovinga, Johanna Anna (2014). The splenic autoimmune response to ADAMTS13 in thrombotic thrombocytopenic purpura contains recurrent antigen-binding CDR3 motifs. Blood, 124(23), pp. 3469-3479. American Society of Hematology 10.1182/blood-2014-04-561142

Adler, Marcel; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard (2014). Le purpura thrombotique thrombocytopénique - un diagtnostic méconnu. Revue médicale suisse, pp. 2280-2284. Médecine & Hygiène

Jiang, Yang; McIntosh, Jennifer J; Reese, Jessica A; Deford, Cassandra C; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; Terrell, Deirdra R; Vesely, Sara K; Knudtson, Eric J; George, James N (2014). Pregnancy outcomes following recovery from acquired thrombotic thrombocytopenic purpura. Blood, 123(11), pp. 1674-80. American Society of Hematology 10.1182/blood-2013-11-538900

Falter, T; Kremer Hovinga, Johanna Anna; Lackner, K; Füllemann, H-G; Lämmle, Bernhard; Scharrer, I (2014). Late onset and pregnancy-induced congenital thrombotic thrombocytopenic purpura. Hämostaseologie, 34(3), pp. 244-248. Schattauer 10.5482/HAMO-14-03-0023

von Krogh, Anne-Sophie; Kremer Hovinga, Johanna Anna; Tjønnfjord, Geir E.; Ringen, Ingrid M.; Lämmle, Bernhard; Waage, Anders; Quist-Paulsen, Petter (2014). The impact of congenital thrombotic thrombocytopenic purpura on pregnancy complications. Thrombosis and haemostasis, 111(6), pp. 1180-1183. Schattauer 10.1160/TH13-08-0713

Rank, Cecilie Utke; Kremer Hovinga, Johanna Anna; Mansouri Taleghani, Magnus; Lämmle, Bernhard; Gøtze, Jens Peter; Nielsen, Ove Juul (2014). Congenital thrombotic thrombocytopenic purpura caused by new compound heterozygous mutations of the ADAMTS13 gene. European journal of haematology, 92(2), pp. 168-171. Wiley-Blackwell 10.1111/ejh.12197

Ferrari, Silvia; Palavra, Kristina; Gruber, Bernadette; Kremer Hovinga, Johanna Anna; Knöbl, Paul; Caron, Claudine; Cromwell, Caroline; Aledort, Louis; Plaimauer, Barbara; Turecek, Peter L.; Rottensteiner, Hanspeter; Scheiflinger, Friedrich (2014). Persistence of circulating ADAMTS13-specific immune complexes in patients with acquired thrombotic thrombocytopenic purpura. Haematologica - the hematology journal, 99(4), pp. 779-787. Ferrata-Storti Foundation 10.3324/haematol.2013.094151

Deford, Cassandra C.; Reese, Jessica A.; Schwartz, Lauren H.; Perdue, Jedidiah J.; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; Terrell, Deirdra R.; Vesely, Sara K.; George, James N. (2013). Multiple major morbidities and increased mortality during long-term follow-up after recovery from thrombotic thrombocytopenic purpura. Blood, 122(12), pp. 2023-2029. American Society of Hematology 10.1182/blood-2013-04-496752

Mansouri Taleghani, Magnus; von Krogh, A.-S.; Fujimura, Y.; George, J. N.; Hrachovinová, I.; Knöbl, P. N.; Quist-Paulsen, P.; Schneppenheim, R.; Lämmle, Bernhard; Kremer Hovinga, Johanna Anna (2013). Hereditary thrombotic thrombocytopenic purpura and the hereditary TTP registry. Hämostaseologie, 33(2), pp. 138-43. Schattauer 10.5482/HAMO-13-04-0026

Kremer Hovinga, Johanna Anna (2013). Thrombotic microangiopathies. Hämostaseologie, 33(2), p. 81. Schattauer

Schaller, Monica; Studt, J.-D.; Voorberg, J.; Kremer Hovinga, Johanna Anna (2013). Acquired thrombotic thrombocytopenic purpura. Development of an autoimmune response. Hämostaseologie, 33(2), pp. 121-30. Schattauer 10.5482/HAMO-12-12-0023

Book Section

Kremer Hovinga, Johanna Anna (2017). Thrombotic thrombocytopenic purpura and hemolytic uremic syndrome. In: Gresele, Paolo; Kleiman, Neal S.; Lopez, José A.; Page, Clive P. (eds.) Platelets in Thrombotic and Non-Thrombotic Disorders (pp. 851-871). Springer 10.1007/978-3-319-47462-5_57

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