"Rapid two-stage" Norwood operation in a child with multiorgan failure

Schmitz, C; Schirrmeister, J; Herberg, U; Kozlik-Feldmann, R; Stüber, F; Welz, A; Breuer, J (2009). "Rapid two-stage" Norwood operation in a child with multiorgan failure. Pediatric cardiology, 30(1), pp. 77-9. New York, N.Y.: Springer Science+Business Media 10.1007/s00246-008-9261-9

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The Norwood I operation continues to be a procedure with significant operative mortality. One well-accepted risk factor for death after the first step of the Norwood operation is critical preoperative status. We describe herein a new concept for the treatment of patients with hypoplastic left heart syndrome (HLHS) in very poor preoperative condition. This is a case report of a child who was born in a rural hospital. On the second day of life he was referred to our center in multiorgan failure. There were signs of liver dysfunction and the child was anuric. Therapy was started immediately with prostaglandin and vasodilators as well as diuretics, milrinone, and dobutamine. However, systemic perfusion continued to be insufficient. Finally, the child was placed on a ventilator. On the fourth day of life, bilateral pulmonary artery (PA) banding was performed and circulation stabilized immediately. Two hours after the operation urine output started. Liver function stabilized over the next couple of days. Two days after PA banding the child was weaned from the ventilator. On the 12th day of life a Norwood operation with PA debanding and a right ventricle-PA conduit was performed, and 2 days postoperatively the child was weaned from the ventilator. Twenty days after the operation he was discharged home. When the boy was 4 months old a bidirectional cavopulmonary anastomosis was performed. In selected cases of patients with HLHS with very poor hemodynamic conditions, a rapid two-stage approach with bilateral banding followed by a Norwood operation after cardiac stabilization can be recommended.

Item Type:

Journal Article (Further Contribution)

Division/Institute:

04 Faculty of Medicine > Department of Intensive Care, Emergency Medicine and Anaesthesiology (DINA) > Clinic and Policlinic for Anaesthesiology and Pain Therapy

UniBE Contributor:

Stüber, Frank

Subjects:

600 Technology > 610 Medicine & health

ISSN:

0172-0643

ISBN:

18626682

Publisher:

Springer Science+Business Media

Language:

English

Submitter:

Factscience Import

Date Deposited:

04 Oct 2013 15:03

Last Modified:

05 Dec 2022 14:19

Publisher DOI:

10.1007/s00246-008-9261-9

PubMed ID:

18626682

Web of Science ID:

000262679400015

BORIS DOI:

10.48350/27298

URI:

https://boris.unibe.ch/id/eprint/27298 (FactScience: 105936)

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