Spontaneous bilateral chylothorax with fatal outcome in a patient with melorheostosis

Leuenberger, Michèle; Braunwalder, Jan; Schmid, Ralph A; Stanga, Zeno (2008). Spontaneous bilateral chylothorax with fatal outcome in a patient with melorheostosis. Saudi medical journal, 29(11), pp. 1666-8. Riyadh: Riyadh Al-Kharj Hospital Programme

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We report a case of progressive, multifocal melorheostosis in a 28-year-old woman, with involvement of the left arm, chest, spine, and impressive soft tissue involvement. In the past, she had undergone multiple vascular interventions. She presented with spontaneous massive bilateral chylothorax. After conservative treatment without success, we conducted bilateral pleurodesis. This resulted in a clear reduction of pleural effusions, but her medical condition subsequently worsened due to progressive parenchymatous infiltrates, and increased interlobal pleural effusions. She ultimately died of global respiratory insufficiency. In patients with melorheostosis, involvement of the soft tissue can result in distinctive morbidity, and whenever possible, treatment should be conservative.

Item Type:

Journal Article (Original Article)

Division/Institute:

04 Faculty of Medicine > Department of Gynaecology, Paediatrics and Endocrinology (DFKE) > Clinic of Endocrinology, Diabetology and Clinical Nutrition
04 Faculty of Medicine > Department of Gastro-intestinal, Liver and Lung Disorders (DMLL) > Clinic of Thoracic Surgery

UniBE Contributor:

Leuenberger, Michèle Simone; Schmid, Ralph and Stanga-Nodari, Zeno

Subjects:

600 Technology > 610 Medicine & health

ISSN:

0379-5284

ISBN:

18998022

Publisher:

Riyadh Al-Kharj Hospital Programme

Language:

English

Submitter:

Factscience Import

Date Deposited:

04 Oct 2013 15:05

Last Modified:

01 Oct 2020 11:33

PubMed ID:

18998022

Web of Science ID:

000262345300026

URI:

https://boris.unibe.ch/id/eprint/28181 (FactScience: 118351)

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