Reversal of cardiomyopathy in propionic acidemia after liver transplantation: a 10-year follow-up

Arrizza, Chiara; De Gottardi, Andrea; Foglia, Ezio; Baumgartner, Matthias; Gautschi, Matthias; Nuoffer, Jean-Marc (2015). Reversal of cardiomyopathy in propionic acidemia after liver transplantation: a 10-year follow-up. Transplant international, 28(12), pp. 1447-1450. Wiley-Blackwell 10.1111/tri.12677

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Cardiomyopathy is a frequent complication in propionic acidemia. It is mostly rapidly fatal and independent of the metabolic control or medical intervention. Here, we present the reversal of a severe cardiomyopathy after liver transplantation in a patient with propionic acidemia and the long-term stability after ten years. Liver transplantation in patients with propionic acidemia may be considered a valid and long-lasting treatment when cardiomyopathy is progressive and unresponsive to medical therapy.

Item Type:

Journal Article (Original Article)

Division/Institute:

04 Faculty of Medicine > Department of Haematology, Oncology, Infectious Diseases, Laboratory Medicine and Hospital Pharmacy (DOLS) > Institute of Clinical Chemistry
04 Faculty of Medicine > Department of Gynaecology, Paediatrics and Endocrinology (DFKE) > Clinic of Paediatric Medicine
04 Faculty of Medicine > Department of Gastro-intestinal, Liver and Lung Disorders (DMLL) > Clinic of Visceral Surgery and Medicine > Hepatology

UniBE Contributor:

Arrizza, Chiara; De Gottardi, Andrea; Gautschi, Matthias and Nuoffer, Jean-Marc

Subjects:

600 Technology > 610 Medicine & health

ISSN:

0934-0874

Publisher:

Wiley-Blackwell

Language:

English

Submitter:

Barbara Keller

Date Deposited:

15 Mar 2016 12:04

Last Modified:

17 Mar 2016 21:58

Publisher DOI:

10.1111/tri.12677

PubMed ID:

26358860

Uncontrolled Keywords:

cardiomyopathy; metabolic decompensation; orthotopic liver transplantation; propionic acidemia

BORIS DOI:

10.7892/boris.76863

URI:

https://boris.unibe.ch/id/eprint/76863

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