Zipponi, Manuel; Eugster, Roland; Birrenbach, Tanja (2011). High-dose intravenous immunoglobulins: A promising therapeutic approach for idiopathic systemic capillary leak syndrome. BMJ case reports, 2011(apr27 1), bcr1220103599-bcr1220103599. London: BMJ Publishing Group 10.1136/bcr.12.2010.3599
Full text not available from this repository.The systemic capillary leak syndrome (SCLS), also known as Clarkson’s disease, is a life-threatening disorder of unknown cause. It is characterised by recurrent acute episodes of hypotension, weight gain and generalised oedema with haemoconcentration and hypoproteinaemia caused by paroxysmal capillary hyperpermeability with a shift of plasma fluid from the intravascular to the interstitial space. We report the case of a 40-year-old woman with chronic SCLS treated with high-dose intravenous immunoglobulins, after a prophylactic therapy with theophylline and terbutaline was poorly tolerated and failed to decrease the frequency and severity of the attacks sufficiently.
Item Type: |
Journal Article (Original Article) |
---|---|
Division/Institute: |
04 Faculty of Medicine > Department of Head Organs and Neurology (DKNS) > Clinic of Neurology > Centre of Competence for Psychosomatic Medicine |
UniBE Contributor: |
Birrenbach, Tanja Nicole |
ISSN: |
1757-790X |
Publisher: |
BMJ Publishing Group |
Language: |
English |
Submitter: |
Factscience Import |
Date Deposited: |
04 Oct 2013 14:23 |
Last Modified: |
07 Jan 2024 00:20 |
Publisher DOI: |
10.1136/bcr.12.2010.3599 |
PubMed ID: |
22696704 |
URI: |
https://boris.unibe.ch/id/eprint/8022 (FactScience: 213436) |