Kremer Hovinga, Johanna Anna

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Journal Article

Liniger, Sophia; Dantonello, Tobias; Diepold, Miriam; Aebi, Christoph; Brodard, Justine; Kremer Hovinga, Johanna A.; Rössler, Jochen Karl; Kartal-Kaess, Mutlu (2022). Severe acquired purpura fulminans in a child. Archives of disease in childhood, 107(3), p. 300. BMJ Publishing Group 10.1136/archdischild-2021-322379

Krzywicka, Katarzyna; van de Munckhof, Anita; Sánchez van Kammen, Mayte; Heldner, Mirjam R; Jood, Katarina; Lindgren, Erik; Tatlisumak, Turgut; Putaala, Jukka; Kremer Hovinga, Johanna A; Middeldorp, Saskia; Levi, Marcel M; Cordonnier, Charlotte; Arnold, Marcel; Zwinderman, Aeilko H; Ferro, José M; Coutinho, Jonathan M; Aguiar de Sousa, Diana (2022). Age-Stratified Risk of Cerebral Venous Sinus Thrombosis After SARS-CoV-2 Vaccination. Neurology, 98(7), e759-e768. American Academy of Neurology 10.1212/WNL.0000000000013148

Van den Berg, Jana; Kremer Hovinga, Johanna A.; Pfleger, Claudia; Hegemann, Inga; Stehle, Gregor Thomas; Holbro, Andreas; Studt, Jan-Dirk (2022). Daratumumab for immune thrombotic thrombocytopenic purpura. Blood advances, 6(3), pp. 993-997. American Society of Hematology 10.1182/bloodadvances.2021005124

van de Munckhof, Anita; Krzywicka, Katarzyna; Aguiar de Sousa, Diana; Sánchez van Kammen, Mayte; Heldner, Mirjam R.; Jood, Katarina; Lindgren, Erik; Tatlisumak, Turgut; Putaala, Jukka; Kremer Hovinga, Johanna A.; Middeldorp, Saskia; Levi, Marcel; Arnold, Marcel; Ferro, José M; Coutinho, Jonathan M (2022). Declining mortality of cerebral venous sinus thrombosis with thrombocytopenia after SARS-CoV-2 vaccination. European journal of neurology, 29(1), pp. 339-344. Wiley 10.1111/ene.15113

Sánchez van Kammen, Mayte; Aguiar de Sousa, Diana; Poli, Sven; Cordonnier, Charlotte; Heldner, Mirjam R.; van de Munckhof, Anita; Krzywicka, Katarzyna; van Haaps, Thijs; Ciccone, Alfonso; Middeldorp, Saskia; Levi, Marcel M; Kremer Hovinga, Johanna A.; Silvis, Suzanne; Hiltunen, Sini; Mansour, Maryam; Arauz, Antonio; Barboza, Miguel A; Field, Thalia S; Tsivgoulis, Georgios; Nagel, Simon; ... (2021). Characteristics and Outcomes of Patients With Cerebral Venous Sinus Thrombosis in SARS-CoV-2 Vaccine-Induced Immune Thrombotic Thrombocytopenia. JAMA neurology, 78(11), pp. 1314-1323. American Medical Association 10.1001/jamaneurol.2021.3619

Krzywicka, Katarzyna; Heldner, Mirjam R.; Sánchez van Kammen, Mayte; van Haaps, Thijs; Hiltunen, Sini; Silvis, Suzanne M; Levi, Marcel; Kremer Hovinga, Johanna A.; Jood, Katarina; Lindgren, Erik; Tatlisumak, Turgut; Putaala, Jukka; Aguiar de Sousa, Diana; Middeldorp, Saskia; Arnold, Marcel; Coutinho, Jonathan M; Ferro, José M (2021). Post-SARS-CoV-2-vaccination Cerebral Venous Sinus Thrombosis: an analysis of cases notified to the European Medicines Agency. European journal of neurology, 28(11), pp. 3656-3662. Wiley 10.1111/ene.15029

Rössler, Jochen Karl; Baumgartner, Iris; Kremer Hovinga, Johanna A. (2021). EHA Endorsement of the Second International Guidelines for the Diagnosis and Management of Hereditary Hemorrhagic Telangiectasia. HemaSphere, 5(11), e647. Wolters Kluwer Health 10.1097/HS9.0000000000000647

Nilius, Henning; Mertins, Tamara; Boss, Robin; Knuchel, Matthias; Blozik, Eva; Kremer Hovinga, Johanna Anna; Eichinger, Sabine; Nagler, Michael (2021). Long-Term Survival After Venous Thromboembolism: A Prospective Cohort Study. Frontiers in cardiovascular medicine, 8(749342), p. 749342. Frontiers 10.3389/fcvm.2021.749342

Sánchez van Kammen, Mayte; Heldner, Mirjam R.; Brodard, Justine; Scutelnic, Adrian; Silvis, Suzanne; Schroeder, Verena; Kremer Hovinga, Johanna A.; Middeldorp, Saskia; Levi, Marcel; Hiltunen, Sini; Lindgren, Erik; Mansour, Maryam; Arauz, Antonio; Barboza, Miguel A.; Zuurbier, Susanna M.; Aguiar de Sousa, Diana; Ferro, Jose M.; Fischer, Urs; Field, Thalia S.; Jood, Katarina; ... (2021). Frequency of Thrombocytopenia and Platelet Factor 4/Heparin Antibodies in Patients With Cerebral Venous Sinus Thrombosis Prior to the COVID-19 Pandemic. JAMA : the journal of the American Medical Association, 326(4), pp. 332-338. American Medical Association 10.1001/jama.2021.9889

Balduini, Carlo; Freson, Kathleen; Greinacher, Andreas; Gresele, Paolo; Kühne, Thomas; Scully, Marie; Bakchoul, Tamam; Coppo, Paul; Dovc Drnovsek, Tadeja; Godeau, Bertrand; Gruel, Yves; Rao, A Koneti; Kremer Hovinga, Johanna A.; Makris, Michael; Matzdorff, Axel; Mumford, Andrew; Pecci, Alessandro; Raslova, Hana; Rivera, José; Roberts, Irene; ... (2021). The EHA Research Roadmap: Platelet Disorders. HemaSphere, 5(7), e601. Wolters Kluwer Health 10.1097/HS9.0000000000000601

Tarasco, Erika; Bütikofer, Lukas; Friedman, Kenneth D; George, James N; Hrachovinova, Ingrid V; Knöbl, Paul; Matsumoto, Masanori; von Krogh, Anne Sophie; Aebi-Huber, Isabella; Cermakova, Zuzana; Górska-Kosicka, Magdalena; Jalowiec, Katarzyna A; Largiadèr, Carlo R; Prohaszka, Zoltan; Sinkovits, György; Windyga, Jerzy; Lämmle, Bernhard; Kremer Hovinga, Johanna A (2021). Annual Incidence and Severity of Acute Episodes in Hereditary Thrombotic Thrombocytopenic Purpura. Blood, 137(25), pp. 3563-3575. American Society of Hematology 10.1182/blood.2020009801

Brodard, Justine; Kremer Hovinga, Johanna A.; Fontana, Pierre; Studt, Jan-Dirk; Gruel, Yves; Greinacher, Andreas (2021). COVID-19 patients often show high-titer non-platelet-activating anti-PF4/heparin IgG antibodies. Journal of thrombosis and haemostasis, 19(5), pp. 1294-1298. Wiley-Blackwell 10.1111/jth.15262

Peyvandi, Flora; Cataland, Spero; Scully, Marie; Coppo, Paul; Knoebl, Paul; Kremer Hovinga, Johanna A.; Metjian, Ara; de la Rubia, Javier; Pavenski, Katerina; Minkue Mi Edou, Jessica; De Winter, Hilde; Callewaert, Filip (2021). Caplacizumab prevents refractoriness and mortality in acquired thrombotic thrombocytopenic purpura: integrated analysis. Blood advances, 5(8), pp. 2137-2141. American Society of Hematology 10.1182/bloodadvances.2020001834

Cuker, Adam; Cataland, Spero R; Coppo, Paul; de la Rubia, Javier; Friedman, Kenneth D; George, James N; Knoebl, Paul N; Kremer Hovinga, Johanna A.; Lämmle, Bernhard; Matsumoto, Masanori; Pavenski, Katerina; Peyvandi, Flora; Sakai, Kazuya; Sarode, Ravi; Thomas, Mari R; Tomiyama, Yoshiaki; Veyradier, Agnès; Westwood, John-Paul; Scully, Marie (2021). Redefining outcomes in immune TTP: an international working group consensus report. Blood, 137(14), pp. 1855-1861. American Society of Hematology 10.1182/blood.2020009150

Esteves Pereira, Michael; Bocksrucker, Christoph; Kremer Hovinga, Johanna Anna; Mueller, Martin; Daskalakis, Michael; Mansouri Taleghani, Behrouz; Nagler, Michael (2021). Immunoadsorption for the Treatment of Acquired Hemophilia: New Observational Data, Systematic Review, and Meta-Analysis. Transfusion medicine reviews, 35(2), pp. 125-134. Elsevier 10.1016/j.tmrv.2021.01.001

De Gaudenzi, Martina; Kremer Hovinga, Johanna A.; Rössler, Jochen; Kaess, Michael; Kartal-Kaess, Mutlu (2021). Psychische Gesundheit bei chronischen Erkrankungen am Beispiel der Hämophilie. Paediatrica, 32(2), pp. 13-16. Schweizerische Gesellschaft für Pädiatrie SGP 10.35190/d2021.2.2

Fontana, Pierre; Alberio, Lorenzo; Albisetti, Manuela; Angelillo, Anne; Asmis, Lars M; Casini, Alessandro; Gerber, Bernhard; Graf, Lukas; Hegemann, Inga; Korte, Wolfgang; Martinez, Maria; Studt, Jan-Dirk; Tsakiris, Dimitrios A; Wuillemin, Walter A; Kremer Hovinga, Johanna A. (2020). Management of bleeding events and invasive procedures in patients with haemophilia A without inhibitors treated with emicizumab. Swiss medical weekly, 150, w20422. EMH Schweizerischer Ärzteverlag 10.4414/smw.2020.20422

Li, Ang; Kremer Hovinga, Johanna A. (2020). Laboratory surveillance of immune-mediated thrombotic thrombocytopenic purpura. Hematology. American Society of Hematology education program, 2020(1), pp. 82-84. American Society of Hematology 10.1182/hematology.2020000164

Mackie, Ian; Mancini, Ilaria; Muia, Joshua; Kremer Hovinga, Johanna; Nair, Sukesh; Machin, Sam; Baker, Ross (2020). International Council for Standardization in Haematology (ICSH) recommendations for laboratory measurement of ADAMTS13. International journal of laboratory hematology, 42(6), pp. 685-696. Wiley 10.1111/ijlh.13295

Kremer Hovinga, Johanna A.; Braschler, Thomas R; Buchkremer, Florian; Farese, Stefan; Hengartner, Heinz; Lovey, Pierre-Yves; Largiadèr, Carlo R.; Mansouri Taleghani, Behrouz; Tarasco, Erika (2020). Insights from the Hereditary Thrombotic Thrombocytopenic Purpura Registry: Discussion of Key Findings Based on Individual Cases from Switzerland. Hämostaseologie, 40(S 01), S5-S14. Thieme 10.1055/a-1282-2264

Jalowiec, Katarzyna A.; Andres, Martin; Mansouri Taleghani, Behrouz; Musa, Albulena; Dickenmann, Martina; Angelillo-Scherrer, Anne; Rovó, Alicia; Kremer Hovinga, Johanna Anna (2020). Acquired hemophilia A and plasma cell neoplasms: a case report and review of the literature. Journal of medical case reports, 14(1), p. 206. BioMed Central 10.1186/s13256-020-02505-7

Barco, Stefano; Sollfrank, Stefanie; Trinchero, Alice; Adenaeuer, Anke; Abolghasemi, Hassan; Conti, Laura; Häuser, Friederike; Kremer Hovinga, Johanna A.; Lackner, Karl J; Loewecke, Felicia; Miloni, Erwin; Vazifeh Shiran, Nader; Tomao, Luigi; Wuillemin, Walter A; Zieger, Barbara; Lämmle, Bernhard; Rossmann, Heidi (2020). Severe plasma prekallikrein deficiency: Clinical characteristics, novel KLKB1 mutations, and estimated prevalence. Journal of thrombosis and haemostasis, 18(7), pp. 1598-1617. Wiley-Blackwell 10.1111/jth.14805

Alberio, Lorenzo A.; Angelillo-Scherrer, Anne; Asmis, Lars M.; Casini, Alessandro; Fontana, Pierre; Graf, Lukas; Hegemann, Inga; Kremer Hovinga, Johanna A.; Korte, Wolfgang; Lecompte, Thomas; Martinez, Martina; Nagler, Michael; Studt, Jan-Dirk; Tsakiris, Dimitrios A.; Wuillemin, Walter A. (2020). Recommendations on the use of anticoagulants for the treatment of patients with heparin-induced thrombocytopenia in Switzerland. Swiss medical weekly, 150(w20210), w20210. EMH Media 10.4414/smw.2020.20210

Casini, Alessandro; Alberio, Lorenzo; Angelillo-Scherrer, Anne; Fontana, Pierre; Gerber, Bernhard; Graf, Lukas; Hegemann, Inga; Korte, Wolfgang; Kremer Hovinga, Johanna A.; Lecompte, Thomas; Martinez, Maria; Nagler, Michael; Studt, Jan-Dirk; Tsakiris, Dimitrios; Wuillemin, Walter; Asmis, Lars (2020). Suggestions for thromboprophylaxis and laboratory monitoring for in-hospital patients with COVID-19 - a Swiss consensus statement by the Working Party Hemostasis. Swiss medical weekly, 150(w20247), w20247. EMH Media 10.4414/smw.2020.20247

Tarasco, E.; Aebi-Huber, I.; Kremer Hovinga, J. A. (2020). Die erbliche Form der thrombotisch thrombozytopenischen Purpura (TTP) – selten, aber bei Schwangerschaftskomplikationen zu bedenken! Vasomed - die Fachzeitschrift für Gefässerkrankungen, 32(3), pp. 90-91. Viavital-Verl.-GmbH

Tarasco, Erika; Aebi-Huber, Isabella; Kremer Hovinga, Johanna A. (2020). The Hereditary TTP Registry: who we are, what we do, why you should join us. Leading Opinions. Hämatologie & Onkologie(3), pp. 6-8. Universimed

Knoebl, Paul; Cataland, Spero; Peyvandi, Flora; Coppo, Paul; Scully, Marie; Kremer Hovinga, Johanna A.; Metjian, Ara; de la Rubia, Javier; Pavenski, Katerina; Minkue Mi Edou, Jessica; De Winter, Hilde; Callewaert, Filip (2020). Efficacy and safety of open-label caplacizumab in patients with exacerbations of acquired thrombotic thrombocytopenic purpura in the HERCULES study. Journal of thrombosis and haemostasis, 18(2), pp. 479-484. Wiley-Blackwell 10.1111/jth.14679

Kremer Hovinga, Johanna A.; George, James N. (2020). Hereditary Thrombotic Thrombocytopenic Purpura. Reply. The New England journal of medicine, 382(4), pp. 394-395. Massachusetts Medical Society 10.1056/NEJMc1915670

Borogovac, Azra; Tarasco, Erika; Kremer Hovinga, Johanna A.; George, James N. (2020). Hypertension in patients with hereditary thrombotic thrombocytopenic purpura. eJHaem, 1(1), pp. 342-343. Wiley 10.1002/jha2.29

Orosz, Zsuzsanna Z; Bárdos, Helga; Shemirani, Amir H; Beke Debreceni, Ildikó; Lassila, Riitta; Riikonen, Antti S; Kremer Hovinga, Johanna A.; Seiler, Theo G.; van Dorland, Hendrika A.; Schroeder, Verena; Boda, Zoltán; Nemes, László; Früh Epstein, Beatrice; Nagy, Bence; Facskó, Andrea; Kappelmayer, János; Muszbek, László (2019). Cellular Factor XIII, a Transglutaminase in Human Corneal Keratocytes. International journal of molecular sciences, 20(23) Molecular Diversity Preservation International MDPI 10.3390/ijms20235963

Schneider, Conrad; Stutz-Grunder, E; Lüer, Sonja; Keller, Heinz Peter; Kremer Hovinga, Johanna Anna; Ammann, R A; Karow, Axel (2019). Fulminant Essential Thrombocythemia Associated with Acquired Von Willebrand Syndrome and Bleeding Episodes in a 14-year-old Girl. Hämostaseologie, 39(4), pp. 404-408. Thieme 10.1055/s-0039-1679929

Kremer Hovinga, Johanna A.; George, James N (2019). Hereditary Thrombotic Thrombocytopenic Purpura. The New England journal of medicine, 381(17), pp. 1653-1662. Massachusetts Medical Society 10.1056/NEJMra1813013

Robertz, Judith; Andres, Martin; Mansouri Taleghani, Behrouz; Koneth, Irene; Binet, Isabelle; Kremer Hovinga, Johanna A. (2019). Obinutuzumab in two patients suffering from immune-mediated thrombotic thrombocytopenic purpura intolerant to rituximab. American journal of hematology, 94(10), E259-E261. Wiley-Liss 10.1002/ajh.25583

van Dorland, Hendrika Anette; Mansouri Taleghani, Magnus; Sakai, Kazuya; Friedman, Kenneth D; George, James N; Hrachovinova, Ingrid; Knöbl, Paul N; von Krogh, Anne Sophie; Schneppenheim, Reinhard; Aebi-Huber, Isabella; Bütikofer, Lukas; Largiadèr, Carlo R.; Cermakova, Zuzana; Kokame, Koichi; Miyata, Toshiyuki; Yagi, Hideo; Terrell, Deirdra R; Vesely, Sara K; Matsumoto, Masanori; Lämmle, Bernhard; ... (2019). The International Hereditary Thrombotic Thrombocytopenic Purpura Registry: Key findings at enrolment until 2017. Haematologica - the hematology journal, 104(10), pp. 2107-2115. Ferrata-Storti Foundation 10.3324/haematol.2019.216796

Angelillo-Scherrer, Anne; Mansouri Taleghani, Behrouz; Förger, Frauke; Baerlocher, Gabriela M.; Pabst, Thomas; Pöllinger, Alexander; Banz, Yara; Geiser, Thomas; Kremer Hovinga, Johanna A.; Rovó, Alicia (2019). Immunoadsorption and autologous transplantation for life-threatening primary antiphospholipid syndrome. Blood advances, 3(17), pp. 2664-2667. American Society of Hematology 10.1182/bloodadvances.2019000465

Tiefenbacher, Stefan; Albisetti, Manuela; Baker, Peter; Kappert, Guenther; Kitchen, Steve; Kremer Hovinga, Johanna A.; Pouplard, Claire; Scholz, Ute; Ternisien, Catherine; Borgvall, Carin; Vicente, Tiago; Belyanskaya, Larisa; Walter, Olaf; Oldenburg, Johannes (2019). Estimation of Nuwiq® (simoctocog alfa) activity using one-stage and chromogenic assays-Results from an international comparative field study. Haemophilia, 25(4), pp. 708-717. Wiley 10.1111/hae.13763

Scully, Marie; Cataland, Spero R; Peyvandi, Flora; Coppo, Paul; Knöbl, Paul; Kremer Hovinga, Johanna A.; Metjian, Ara; de la Rubia, Javier; Pavenski, Katerina; Callewaert, Filip; Biswas, Debjit; De Winter, Hilde; Zeldin, Robert K (2019). Caplacizumab Treatment for Acquired Thrombotic Thrombocytopenic Purpura. The New England journal of medicine, 380(4), pp. 335-346. Massachusetts Medical Society 10.1056/NEJMoa1806311

Schmid, Manuela; Spichiger, Elisabeth; Kremer Hovinga, Johanna Anna (2019). Aufbau einer interprofessionellen Betreuung für Patientinnen/Patienten mit angeborenen Hämostasestörungen (In Press). Pflegewissenschaft H P S Media 10.3936/1588

Kremer Hovinga, Johanna Anna; Heeb, Silvan Rolf; Skowronska, Magdalena; Schaller Tschan, Monica Maria (2018). Pathophysiology of thrombotic thrombocytopenic purpura and hemolytic uremic syndrome. Journal of thrombosis and haemostasis, 16(4), pp. 618-629. Wiley-Blackwell 10.1111/jth.13956

Prince Eladnani, Raja; Bologna, Luca; Manetti, Mirko; Melchiorre, Daniela; Rosa, Irene; Dewarrat, Natacha; Suardi, Silvia; Amini, Poorya; Fernández, José A; Burnier, Laurent; Quarroz, Claudia; Reina Caro, Maria Desiré; Matsumura, Yasuhiro; Kremer Hovinga, Johanna Anna; Griffin, John H; Simon, Hans-Uwe; Ibba-Manneschi, Lidia; Saller, François; Calzavarini, Sara and Angelillo, Anne (2018). Targeting anticoagulant protein S to improve hemostasis in hemophilia. Blood, 131(12), pp. 1360-1371. American Society of Hematology 10.1182/blood-2017-09-800326

Scully, Marie; Knöbl, Paul; Kentouche, Karim; Rice, Lawrence; Windyga, Jerzy; Schneppenheim, Reinhard; Kremer Hovinga, Johanna Anna; Kajiwara, Michiko; Fujimura, Yoshihiro; Maggiore, Caterina; Doralt, Jennifer; Hibbard, Christopher; Martell, Leah; Ewenstein, Bruce (2017). A recombinant human ADAMTS-13: first-in-human study evaluating pharmacokinetics, safety and tolerability in cTTP patients. Blood, 130(19), pp. 2055-2063. American Society of Hematology 10.1182/blood-2017-06-788026

Peyvandi, F; Scully, M; Kremer Hovinga, Johanna Anna; Knöbl, P; Cataland, S; De Beuf, K; Callewaert, F; De Winter, H; Zeldin, R K (2017). Caplacizumab reduces the frequency of major thromboembolic events, exacerbations, and death in patients with acquired thrombotic thrombocytopenic purpura. Journal of thrombosis and haemostasis, 15(7), pp. 1448-1452. Wiley-Blackwell 10.1111/jth.13716

Page, Evaren E; Kremer Hovinga, Johanna Anna; Terrell, Deirdra R; Vesely, Sara K; George, James N (2017). Thrombotic thrombocytopenic purpura: diagnostic criteria, clinical features, and long-term outcomes from 1995 through 2015. Blood advances, 1(10), pp. 590-600. American Society of Hematology 10.1182/bloodadvances.2017005124

Kremer Hovinga, Johanna Anna; Coppo, Paul; Lämmle, Bernhard; Moake, Joel L; Miyata, Toshiyuki; Vanhoorelbeke, Karen (2017). Thrombotic thrombocytopenic purpura. Nature reviews. Disease Primers, 3(17020), p. 17020. Nature Publishing Group 10.1038/nrdp.2017.20

Kremer Hovinga, Johanna Anna; Scharf, Rüdiger E (2017). Progress in Haemostasis. From individual patients to pathophysiological insights. Hämostaseologie, 37(1), pp. 9-11. Schattauer

Scully, M; Cataland, S; Coppo, P; de la Rubia, J; Friedman, K D; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; Matsumoto, M; Pavenski, K; Sadler, E; Sarode, R; Wu, H (2017). Consensus on the standardization of terminology in thrombotic thrombocytopenic purpura and related thrombotic microangiopathies. Journal of thrombosis and haemostasis, 15(2), pp. 312-322. Wiley-Blackwell 10.1111/jth.13571

Kölm, Robert; Schaller Tschan, Monica; Roumenina, Lubka T; Niemiec, Iga; Kremer Hovinga, Johanna Anna; Khanicheh, Elham; Kaufmann, Beat A; Hopfer, Helmut; Trendelenburg, Marten (2016). Von Willebrand Factor Interacts with Surface-Bound C1q and Induces Platelet Rolling. Journal of immunology, 197(9), pp. 3669-3679. American Association of Immunologists 10.4049/jimmunol.1501876

Page, Evaren E; Kremer Hovinga, Johanna Anna; Terrell, Deirdra R; Vesely, Sara K; George, James N (2016). Clinical importance of ADAMTS13 activity during remission in patients with acquired thrombotic thrombocytopenic purpura. Blood, 128(17), pp. 2175-2178. American Society of Hematology 10.1182/blood-2016-06-724161

Nagler, Michael; Kremer Hovinga, Johanna Anna; Alberio, Lorenzo; Peter-Salonen, Kristiina; von Tengg-Kobligk, Hendrik; Lottaz, Daniel; Neerman-Arbez, Marguerite; Lämmle, Bernhard (2016). Thromboembolism in patients with congenital afibrinogenaemia. Long-term observational data and systematic review. Thrombosis and haemostasis, 116(4), pp. 722-732. Schattauer 10.1160/TH16-02-0082

Pavenski, Katerina; Cataland, Spero; Kremer Hovinga, Johanna Anna; Thomas, Mari; Vanhoorelbeke, Karen (2016). Thrombotic thrombocytopenic pupura (TTP) dinner symposium proceedings. Expert review of hematology, 9(8), pp. 733-735. Expert Reviews 10.1080/17474086.2016.1198895

Pedrazzini, Giovanni; Biasco, Luigi; Sulzer, Irmela; Anesini, Adriana; Moccetti, Tiziano; Kremer Hovinga, Johanna Anna; Alberio, Lorenzo (2016). Acquired intracoronary ADAMTS13 deficiency and VWF retention at sites of critical coronary stenosis in patients with STEMI. Blood, 127(23), pp. 2934-2936. American Society of Hematology 10.1182/blood-2015-12-688010

Page, Evaren E; Kremer Hovinga, Johanna Anna; Terrell, Deirdra R; Vesely, Sara K; George, James N (2016). Rituximab reduces risk for relapse in patients with thrombotic thrombocytopenic purpura. Blood, 127(24), pp. 3092-3094. American Society of Hematology 10.1182/blood-2016-03-703827

Fan, Xinping; Kremer Hovinga, Johanna Anna; Shirotani-Ikejima, Hiroko; Eura, Yuka; Hirai, Hidenori; Honda, Shigenori; Kokame, Koichi; Mansouri Taleghani, Magnus; von Krogh, Anne-Sophie; Yoshida, Yoko; Fujimura, Yoshihiro; Lämmle, Bernhard; Miyata, Toshiyuki (2016). Genetic variations in complement factors in patients with congenital thrombotic thrombocytopenic purpura with renal insufficiency. International journal of hematology, 103(3), pp. 283-291. Springer 10.1007/s12185-015-1933-7

Peyvandi, Flora; Scully, Marie; Kremer Hovinga, Johanna Anna; Cataland, Spero; Knöbl, Paul; Wu, Haifeng; Artoni, Andrea; Westwood, John-Paul; Mansouri Taleghani, Magnus; Jilma, Bernd; Callewaert, Filip; Ulrichts, Hans; Duby, Christian; Tersago, Dominique (2016). Caplacizumab for Acquired Thrombotic Thrombocytopenic Purpura. New England journal of medicine NEJM, 374(6), pp. 511-522. Massachusetts Medical Society MMS 10.1056/NEJMoa1505533

von Krogh, A S; Quist-Paulsen, P; Waage, A; Langseth, Ø O; Thorstensen, K; Brudevold, R; Tjønnfjord, G E; Largiadèr, Carlo Rodolfo; Lämmle, Bernhard; Kremer Hovinga, Johanna Anna (2016). High prevalence of hereditary thrombotic thrombocytopenic purpura in Central Norway: from clinical observation to evidence. Journal of thrombosis and haemostasis, 14(1), pp. 73-82. Wiley-Blackwell 10.1111/jth.13186

Kremer Hovinga, Johanna Anna (2016). 111 années après Alexis Nikolaïevitch Romanov, guérison de l’hémophilie B sévère en perspective. Schweizerisches Medizin-Forum SMF / Swiss medical forum / Forum médical suisse FMS, 16(1), pp. 9-11. EMH Editores Medicorum Helveticorum

von Krogh, Anne-Sophie; Kremer Hovinga, Johanna Anna; Romundstad, Pål R; Roten, Linda T; Lämmle, Bernhard; Waage, Anders; Quist-Paulsen, Petter (2015). ADAMTS13 gene variants and function in women with preeclampsia: a population- based nested case- control study from the HUNT Study. Thrombosis research, 136(2), pp. 282-288. Elsevier 10.1016/j.thromres.2015.06.022

Hubbard, A R; Heath, A B; Kremer Hovinga, Johanna Anna (2015). Establishment of the WHO 1st International Standard ADAMTS13, plasma (12/252): communication from the SSC of the ISTH. Journal of thrombosis and haemostasis, 13(6), pp. 1151-1153. Wiley-Blackwell 10.1111/jth.12881

Arni, Delphine; Gumy-Pause, Fabienne; Ansari, Marc; Kremer Hovinga, Johanna Anna; McLin, Valérie A (2015). Successful liver transplantation in a child with acute-on-chronic liver failure and acquired thrombotic thrombocytopenic purpura. Liver transplantation, 21(5), pp. 704-706. Wiley 10.1002/lt.24096

von Auer, Charis; von Krogh, Anne-Sophie; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard (2015). Current insights into thrombotic microangiopathies: Thrombotic thrombocytopenic purpura and pregnancy. Thrombosis research, 135(Suppl1), S30-S33. Elsevier 10.1016/S0049-3848(15)50437-4

Raval, Jay S.; Padmanabhan, Anand; Kremer Hovinga, Johanna Anna; Kiss, Joseph E. (2015). Development of a clinically significant ADAMTS13 inhibitor in a patient with hereditary thrombotic thrombocytopenic purpura. American journal of hematology, 90(1), E22-E22. Wiley-Liss 10.1002/ajh.23851

Jiménez-Alcázar, M; Napirei, M; Panda, R; Köhler, E C; Kremer Hovinga, Johanna Anna; Mannherz, H G; Peine, S; Renné, T; Lämmle, Bernhard; Fuchs, T A (2015). Impaired DNase1-mediated degradation of neutrophil extracellular traps is associated with acute thrombotic microangiopathies. Journal of thrombosis and haemostasis, 13(5), pp. 732-742. Wiley-Blackwell 10.1111/jth.12796

Edgar, Contessa E; Terrell, Deirdra R; Vesely, Sara K; Wren, Jonathan D; Dozmorov, Igor M; Niewold, Timothy B; Brown, Michael; Zhou, Fang; Frank, Mark Barton; Merrill, Joan T; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; James, Judith A; George, James N; Farris, A Darise (2015). Ribosomal and Immune Transcripts Associate with Relapse in Acquired ADAMTS13-Deficient Thrombotic Thrombocytopenic Purpura. PLoS ONE, 10(2), e0117614. Public Library of Science 10.1371/journal.pone.0117614

Schaller Tschan, Monica; Vogel, Monique; Kentouche, Karim; Lämmle, Bernhard; Kremer Hovinga, Johanna Anna (2014). The splenic autoimmune response to ADAMTS13 in thrombotic thrombocytopenic purpura contains recurrent antigen-binding CDR3 motifs. Blood, 124(23), pp. 3469-3479. American Society of Hematology 10.1182/blood-2014-04-561142

Adler, Marcel; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard (2014). Le purpura thrombotique thrombocytopénique - un diagtnostic méconnu. Revue médicale suisse, pp. 2280-2284. Médecine & Hygiène

Jiang, Yang; McIntosh, Jennifer J; Reese, Jessica A; Deford, Cassandra C; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; Terrell, Deirdra R; Vesely, Sara K; Knudtson, Eric J; George, James N (2014). Pregnancy outcomes following recovery from acquired thrombotic thrombocytopenic purpura. Blood, 123(11), pp. 1674-80. American Society of Hematology 10.1182/blood-2013-11-538900

Falter, T; Kremer Hovinga, Johanna Anna; Lackner, K; Füllemann, H-G; Lämmle, Bernhard; Scharrer, I (2014). Late onset and pregnancy-induced congenital thrombotic thrombocytopenic purpura. Hämostaseologie, 34(3), pp. 244-248. Schattauer 10.5482/HAMO-14-03-0023

von Krogh, Anne-Sophie; Kremer Hovinga, Johanna Anna; Tjønnfjord, Geir E.; Ringen, Ingrid M.; Lämmle, Bernhard; Waage, Anders; Quist-Paulsen, Petter (2014). The impact of congenital thrombotic thrombocytopenic purpura on pregnancy complications. Thrombosis and haemostasis, 111(6), pp. 1180-1183. Schattauer 10.1160/TH13-08-0713

Rank, Cecilie Utke; Kremer Hovinga, Johanna Anna; Mansouri Taleghani, Magnus; Lämmle, Bernhard; Gøtze, Jens Peter; Nielsen, Ove Juul (2014). Congenital thrombotic thrombocytopenic purpura caused by new compound heterozygous mutations of the ADAMTS13 gene. European journal of haematology, 92(2), pp. 168-171. Wiley-Blackwell 10.1111/ejh.12197

Ferrari, Silvia; Palavra, Kristina; Gruber, Bernadette; Kremer Hovinga, Johanna Anna; Knöbl, Paul; Caron, Claudine; Cromwell, Caroline; Aledort, Louis; Plaimauer, Barbara; Turecek, Peter L.; Rottensteiner, Hanspeter; Scheiflinger, Friedrich (2014). Persistence of circulating ADAMTS13-specific immune complexes in patients with acquired thrombotic thrombocytopenic purpura. Haematologica - the hematology journal, 99(4), pp. 779-787. Ferrata-Storti Foundation 10.3324/haematol.2013.094151

Diaz, Jose Antonio; Fuchs, Tobias A.; Jackson, Tatum O.; Kremer Hovinga, Johanna A.; Lämmle, Bernhard; Henke, Peter K.; Myers, Daniel D.; Wagner, Denisa D.; Wakefield, Thomas W.; Michigan Research Venous Group, for the (2013). Plasma DNA is Elevated in Patients with Deep Vein Thrombosis. Journal of vascular surgery. Venous and lymphatic disorders, 1(4), 341-348.e1. Elsevier 10.1016/j.jvsv.2012.12.002

Reese, Jessica A.; Muthurajah, Darrshini S.; Kremer Hovinga, Johanna A.; Vesely, Sara K.; Terrell, Deirdra R.; George, James N. (2013). Children and adults with thrombotic thrombocytopenic purpura associated with severe, acquired Adamts13 deficiency: comparison of incidence, demographic and clinical features. Pediatric blood & cancer, 60(10), pp. 1676-1682. Wiley-Liss 10.1002/pbc.24612

Deford, Cassandra C.; Reese, Jessica A.; Schwartz, Lauren H.; Perdue, Jedidiah J.; Kremer Hovinga, Johanna Anna; Lämmle, Bernhard; Terrell, Deirdra R.; Vesely, Sara K.; George, James N. (2013). Multiple major morbidities and increased mortality during long-term follow-up after recovery from thrombotic thrombocytopenic purpura. Blood, 122(12), pp. 2023-2029. American Society of Hematology 10.1182/blood-2013-04-496752

Deal, Taylor; Kremer Hovinga, Johanna A.; Marques, Marisa B.; Adamski, Jill (2013). Novel ADAMTS13 mutations in an obstetric patient with upshaw-schulman syndrome. Journal of clinical apheresis, 28(4), pp. 311-316. New York, N.Y.: Wiley-Liss 10.1002/jca.21251

Mansouri Taleghani, Magnus; von Krogh, A.-S.; Fujimura, Y.; George, J. N.; Hrachovinová, I.; Knöbl, P. N.; Quist-Paulsen, P.; Schneppenheim, R.; Lämmle, Bernhard; Kremer Hovinga, Johanna Anna (2013). Hereditary thrombotic thrombocytopenic purpura and the hereditary TTP registry. Hämostaseologie, 33(2), pp. 138-43. Schattauer 10.5482/HAMO-13-04-0026

Kremer Hovinga, Johanna Anna (2013). Thrombotic microangiopathies. Hämostaseologie, 33(2), p. 81. Schattauer

Schaller, Monica; Studt, J.-D.; Voorberg, J.; Kremer Hovinga, Johanna Anna (2013). Acquired thrombotic thrombocytopenic purpura. Development of an autoimmune response. Hämostaseologie, 33(2), pp. 121-30. Schattauer 10.5482/HAMO-12-12-0023

Hausammann, Stefanie; Vogel, Monique; Kremer Hovinga, Johanna A.; Lacroix-Desmazes, Sebastien; Stadler, Beda M.; Horn, Michael P. (2013). Designed ankyrin repeat proteins: a new approach to mimic complex antigens for diagnostic purposes? PLoS ONE, 8(4), e60688. Public Library of Science 10.1371/journal.pone.0060688

Du, Vivian X; van Os, Gwen; Kremer Hovinga, Johanna A; Dienava-Verdoold, Ilze; Wollersheim, Jacques; Ruggeri, Zaverio M; Fijnheer, Rob; de Groot, Philip G; de Laat, Bas (2012). Indications for a protective function of beta2-glycoprotein I in thrombotic thrombocytopenic purpura. British journal of haematology, 159(1), pp. 94-103. Oxford: Wiley-Blackwell 10.1111/bjh.12004

Fuchs, Tobias A; Kremer Hovinga, Johanna A; Schatzberg, Daphne; Wagner, Denisa D; Lämmle, Bernhard (2012). Circulating DNA and myeloperoxidase indicate disease activity in patients with thrombotic microangiopathies. Blood, 120(6), pp. 1157-64. Washington, D.C.: American Society of Hematology 10.1182/blood-2012-02-412197

Kremer Hovinga, Johanna A; Voorberg, Jan (2012). Improving on nature: redesigning ADAMTS13. Blood, 119(16), pp. 3654-5. Washington, D.C.: American Society of Hematology 10.1182/blood-2012-02-410431

Som, Sumit; Deford, Cassandra C; Kaiser, Mandi L; Terrell, Deirdra R; Kremer Hovinga, Johanna A; Lämmle, Bernhard; George, James N; Vesely, Sara K (2012). Decreasing frequency of plasma exchange complications in patients treated for thrombotic thrombocytopenic purpura-hemolytic uremic syndrome, 1996 to 2011. Transfusion, 52(12), 2525-32; quiz 2524. Malden, Mass.: Wiley-Blackwell 10.1046/j.1537-2995.2000.40080896.x

George, James N; Terrell, Deirdra R; Vesely, Sara K; Kremer Hovinga, Johanna A; Lämmle, Bernhard (2012). Thrombotic microangiopathic syndromes associated with drugs, HIV infection, hematopoietic stem cell transplantation and cancer. Presse médicale, 41(3 Pt 2), e177-88. Issy-les-Moulineaux (F): Elsevier Masson SAS 10.1016/j.lpm.2011.10.026

Kremer Hovinga, Johanna A; Lämmle, Bernhard (2012). Role of ADAMTS13 in the pathogenesis, diagnosis, and treatment of thrombotic thrombocytopenic purpura. Hematology, 2012, pp. 610-616. Washington, D.C.: American Society of Hematology 10.1182/asheducation-2012.1.610

Froehlich-Zahnd, Rahel; George, James N; Vesely, Sara K; Terrell, Deirdra R; Aboulfatova, Khatira; Dong, Jing-Fei; Luken, Brenda M; Voorberg, Jan; Budde, Ulrich; Sulzer, Irmela; Lämmle, Bernhard; Kremer Hovinga, Johanna A (2011). Evidence for a role of anti-ADAMTS13 autoantibodies despite normal ADAMTS13 activity in recurrent thrombotic thrombocytopenic purpura. Haematologica - the hematology journal, 97(2), pp. 297-303. Pavia: Ferrata-Storti Foundation

Jahns, Maximilian; Friess, Dorothea; Demarmels Biasiutti, Franziska; Kremer Hovinga, Johanna A; Alberio, Lorenzo; Oldenburg, Johannes; Lämmle, Bernhard; Colucci, Giuseppe (2011). Massive muscle haematoma three months after starting vitamin K antagonist therapy for deep-vein thrombosis in an antithrombin deficient patient: another case of factor IX propeptide mutation. Thrombosis and haemostasis, 106(2), pp. 381-2. Stuttgart: Schattauer 10.1160/TH11-03-0191

Terrell, Deirdra R; Motto, David G; Kremer Hovinga, Johanna A; Lämmle, Bernhard; George, James N; Vesely, Sara K (2011). Blood group O and black race are independent risk factors for thrombotic thrombocytopenic purpura associated with severe ADAMTS13 deficiency. Transfusion, 51(10), pp. 2237-43. Malden, Mass.: Wiley-Blackwell 10.1111/j.1537-2995.2011.03125.x

Plaimauer, B; Kremer Hovinga, J A; Juno, C; Wolfsegger, M J; Skalicky, S; Schmidt, M; Grillberger, L; Hasslacher, M; Knöbl, P; Ehrlich, H; Scheiflinger, F (2011). Recombinant ADAMTS13 normalizes von Willebrand factor-cleaving activity in plasma of acquired TTP patients by overriding inhibitory antibodies. Journal of thrombosis and haemostasis, 9(5), pp. 936-44. Oxford: Wiley-Blackwell 10.1111/j.1538-7836.2011.04224.x

Pos, W; Luken, B M; Sorvillo, N; Hovinga, J A Kremer; Voorberg, J (2011). Humoral immune response to ADAMTS13 in acquired thrombotic thrombocytopenic purpura. Journal of thrombosis and haemostasis, 9(7), pp. 1285-91. Oxford: Wiley-Blackwell 10.1111/j.1538-7836.2011.04307.x

Terrell, Deirdra R; Vesely, Sara K; Hovinga, Johanna A Kremer; Lämmle, Bernhard; George, James N (2010). Different disparities of gender and race among the thrombotic thrombocytopenic purpura and hemolytic-uremic syndromes. American journal of hematology, 85(11), pp. 844-7. New York, N.Y.: Wiley-Liss 10.1002/ajh.21833

Hovinga, Johanna A Kremer; Vesely, Sara K; Terrell, Deirdra R; Lämmle, Bernhard; George, James N (2010). Survival and relapse in patients with thrombotic thrombocytopenic purpura. Blood, 115(8), 1500-11; quiz 1662. Washington, D.C.: American Society of Hematology 10.1182/blood-2009-09-243790

Benjamin, Melody; Terrell, Deirdra R; Vesely, Sara K; Voskuhl, Gene W; Dezube, Bruce J; Kremer Hovinga, Johanna A; Lämmle, Bernhard; George, James N (2009). Frequency and significance of HIV infection among patients diagnosed with thrombotic thrombocytopenic purpura. Clinical infectious diseases, 48(8), pp. 1129-37. Cary, N.C.: The University of Chicago Press 10.1086/597471

Kennedy, April S; Lewis, Qurana F; Scott, James G; Kremer Hovinga, Johanna A; Lämmle, Bernhard; Terrell, Deirdra R; Vesely, Sara K; George, James N (2009). Cognitive deficits after recovery from thrombotic thrombocytopenic purpura. Transfusion, 49(6), pp. 1092-101. Malden, Mass.: Wiley-Blackwell 10.1111/j.1537-2995.2009.02101.x

Swisher, Karen K; Terrell, Deirdra R; Vesely, Sara K; Kremer Hovinga, Johanna A; Lämmle, Bernhard; George, James N (2009). Clinical outcomes after platelet transfusions in patients with thrombotic thrombocytopenic purpura. Transfusion, 49(5), pp. 873-87. Malden, Mass.: Wiley-Blackwell 10.1111/j.1537-2995.2008.02082.x

Ferrari, S; Mudde, G C; Rieger, M; Veyradier, A; Kremer Hovinga, J A; Scheiflinger, F (2009). IgG subclass distribution of anti-ADAMTS13 antibodies in patients with acquired thrombotic thrombocytopenic purpura. Journal of thrombosis and haemostasis, 7(10), pp. 1703-10. Oxford: Wiley-Blackwell 10.1111/j.1538-7836.2009.03568.x

Pos, W; Luken, B M; Hovinga, J A Kremer; Turenhout, E A M; Scheiflinger, F; Dong, J-F; Fijnheer, R; Voorberg, J (2009). VH1-69 germline encoded antibodies directed towards ADAMTS13 in patients with acquired thrombotic thrombocytopenic purpura. Journal of thrombosis and haemostasis, 7(3), pp. 421-8. Oxford: Wiley-Blackwell 10.1111/j.1538-7836.2008.03250.x

Bergmann, I P; Kremer Hovinga, J A; Lämmle, B; Peter, H J; Schiemann, U (2008). Acute pancreatitis and thrombotic thrombocytopenic purpura. European journal of medical research, 13(10), pp. 481-2. München: I. Holzapfel

Tripodi, A; Peyvandi, F; Chantarangkul, V; Palla, R; Afrasiabi, A; Canciani, M T; Chung, D W; Ferrari, S; Fujimura, Y; Karimi, M; Kokame, K; Kremer Hovinga, J A; Lämmle, B; de Meyer, S F; Plaimauer, B; Vanhoorelbeke, K; Varadi, K; Mannucci, P M (2008). Second international collaborative study evaluating performance characteristics of methods measuring the von Willebrand factor cleaving protease (ADAMTS-13). Journal of thrombosis and haemostasis, 6(9), pp. 1534-41. Oxford: Blackwell 10.1111/j.1538-7836.2008.03099.x

Karpac, Charity A; Li, Xiaoning; Terrell, Deirdra R; Kremer Hovinga, Johanna A; Lämmle, Bernhard; Vesely, Sara K; George, James N (2008). Sporadic bloody diarrhoea-associated thrombotic thrombocytopenic purpura-haemolytic uraemic syndrome: an adult and paediatric comparison. British journal of haematology, 141(5), pp. 696-707. Oxford: Wiley-Blackwell 10.1111/j.1365-2141.2008.07116.x

Lämmle, Bernhard; Kremer Hovinga, Johanna A; George, James N (2008). Acquired thrombotic thrombocytopenic purpura: ADAMTS13 activity, anti-ADAMTS13 autoantibodies and risk of recurrent disease. Haematologica - the hematology journal, 93(2), pp. 172-7. Pavia: Ferrata-Storti Foundation 10.3324/haemato.12701

Meyer, Sara C; Jeddi, Ramzi; Meddeb, Balkis; Gouider, Emna; Lämmle, Bernhard; Kremer Hovinga, Johanna A (2008). A first case of congenital TTP on the African continent due to a new homozygous mutation in the catalytic domain of ADAMTS13. Annals of hematology, 87(8), pp. 663-6. Berlin: Springer 10.1007/s00277-008-0496-6

George, James N; Kremer Hovinga, Johanna A; Terrell, Deirdra R; Vesely, Sara K; Lämmle, Bernhard (2008). The Oklahoma Thrombotic Thrombocytopenic Purpura-Hemolytic Uremic Syndrome Registry: the Swiss connection. European journal of haematology, 80(4), pp. 277-86. Oxford: Wiley-Blackwell 10.1111/j.1600-0609.2008.01040.x

Kremer Hovinga, Johanna A; Meyer, Sara C (2008). Current management of thrombotic thrombocytopenic purpura. Current opinion in hematology, 15(5), pp. 445-50. Hagerstown, Md.: Wolters Kluwer Lippincott Williams & Wilkins 10.1097/MOH.0b013e328309ec62

Rüfer, Axel; Brodmann, Doreen; Gregor, Michael; Kremer Hovinga, Johanna A; Lämmle, Bernhard; Wuillemin, Walter A (2007). Rituximab for acute plasma-refractory thrombotic thrombocytopenic purpura. A case report and concise review of the literature. Swiss medical weekly, 137(37-38), pp. 518-24. Muttenz: EMH Schweizerischer Ärzteverlag

Kremer Hovinga, J A; Zeerleder, S; Kessler, P; Romani de Wit, T; van Mourik, J A; Hack, C E; ten Cate, H; Reitsma, P H; Wuillemin, W A; Lämmle, B (2007). ADAMTS-13, von Willebrand factor and related parameters in severe sepsis and septic shock. Journal of thrombosis and haemostasis, 5(11), pp. 2284-90. Oxford: Blackwell 10.1111/j.1538-7836.2007.02743.x

Swisher, Karen K; Doan, John T; Vesely, Sara K; Kwaan, Hau C; Kim, Benjamin; Laemmle, Bernhard; Kremer Hovinga, Johanna A; George, James N (2007). Pancreatitis preceding acute episodes of thrombotic thrombocytopenic purpura-hemolytic uremic syndrome: report of five patients with a systematic review of published reports. Haematologica - the hematology journal, 92(7), pp. 936-43. Pavia: Ferrata-Storti Foundation 10.3324/haematol.10963

Meyer, S C; Sulzer, I; Lämmle, B; Kremer Hovinga, J A (2007). Hyperbilirubinemia interferes with ADAMTS-13 activity measurement by FRETS-VWF73 assay: diagnostic relevance in patients suffering from acute thrombotic microangiopathies. Journal of thrombosis and haemostasis, 5(4), pp. 866-7. Oxford: Blackwell 10.1111/j.1538-7836.2007.02438.x

Lämmle, B; Kremer Hovinga, J A (2006). A new tool to further explore the role of ADAMTS-13 in health and disease. Journal of thrombosis and haemostasis, 4(5), pp. 952-4. Oxford: Blackwell 10.1111/j.1538-7836.2006.01945.x

Fontana, S; Kremer Hovinga, J A; Lämmle, B; Mansouri Taleghani, B (2006). Treatment of thrombotic thrombocytopenic purpura. Vox sanguinis, 90(4), pp. 245-54. Oxford: Wiley-Blackwell 10.1111/j.1423-0410.2006.00747.x

Kremer Hovinga, J A; Mottini, M; Lämmle, B (2006). Measurement of ADAMTS-13 activity in plasma by the FRETS-VWF73 assay: comparison with other assay methods. Journal of thrombosis and haemostasis, 4(5), pp. 1146-8. Oxford: Blackwell 10.1111/j.1538-7836.2006.01904.x

Luken, B M; Kaijen, P H P; Turenhout, E A M; Kremer Hovinga, J A; van Mourik, J A; Fijnheer, R; Voorberg, J (2006). Multiple B-cell clones producing antibodies directed to the spacer and disintegrin/thrombospondin type-1 repeat 1 (TSP1) of ADAMTS13 in a patient with acquired thrombotic thrombocytopenic purpura. Journal of thrombosis and haemostasis, 4(11), pp. 2355-64. Oxford: Blackwell 10.1111/j.1538-7836.2006.02164.x

Schneppenheim, Reinhard; Kremer Hovinga, Johanna A; Becker, Tim; Budde, Ulrich; Karpman, Diana; Brockhaus, Wolfgang; Hrachovinová, Ingrid; Korczowski, Bartosz; Oyen, Florian; Rittich, Simon; von Rosen, Johannes; Tjønnfjord, Geir E; Pimanda, John E; Wienker, Thomas F; Lämmle, Bernhard (2006). A common origin of the 4143insA ADAMTS13 mutation. Thrombosis and haemostasis, 96(1), pp. 3-6. Stuttgart: Schattauer 10.1160/TH05-12-0817

Schnog, JJ; Hovinga, JA; Krieg, S; Akin, S; Lämmle, B; Brandjes, DP; Mac Gillavry, MR; Muskiet, FD; Duits, AJ; CURAMA, Study Group (2006). ADAMTS13 activity in sickle cell disease. American journal of hematology, 81(7), pp. 492-8. New York, N.Y.: Wiley-Liss 10.1002/ajh.20653

Book Section

Kremer Hovinga, Johanna Anna (2017). Thrombotic thrombocytopenic purpura and hemolytic uremic syndrome. In: Gresele, Paolo; Kleiman, Neal S.; Lopez, José A.; Page, Clive P. (eds.) Platelets in Thrombotic and Non-Thrombotic Disorders (pp. 851-871). Springer 10.1007/978-3-319-47462-5_57

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