Manifestation of a sellar hemangioblastoma due to pituitary apoplexy: a case report

Schär, Ralph; Vajtai, Istvan; Sahli, Rahel; Seiler, Rolf W. (2011). Manifestation of a sellar hemangioblastoma due to pituitary apoplexy: a case report. Journal of medical case reports, 5(496), p. 496. London: BioMed Central 10.1186/1752-1947-5-496

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Introduction Hemangioblastomas are rare, benign tumors occurring in any part of the nervous system. Most are found as sporadic tumors in the cerebellum or spinal cord. However, these neoplasms are also associated with von Hippel-Lindau disease. We report a rare case of a sporadic sellar hemangioblastoma that became symptomatic due to pituitary apoplexy. Case presentation An 80-year-old, otherwise healthy Caucasian woman presented to our facility with severe headache attacks, hypocortisolism and blurred vision. A magnetic resonance imaging scan showed an acute hemorrhage of a known, stable and asymptomatic sellar mass lesion with chiasmatic compression accounting for our patient's acute visual impairment. The tumor was resected by a transnasal, transsphenoidal approach and histological examination revealed a capillary hemangioblastoma (World Health Organization grade I). Our patient recovered well and substitutional therapy was started for panhypopituitarism. A follow-up magnetic resonance imaging scan performed 16 months postoperatively showed good chiasmatic decompression with no tumor recurrence. Conclusions A review of the literature confirmed supratentorial locations of hemangioblastomas to be very unusual, especially within the sellar region. However, intrasellar hemangioblastoma must be considered in the differential diagnosis of pituitary apoplexy.

Item Type:

Journal Article (Original Article)

Division/Institute:

04 Faculty of Medicine > Department of Head Organs and Neurology (DKNS) > Clinic of Neurosurgery
04 Faculty of Medicine > Service Sector > Institute of Pathology
04 Faculty of Medicine > Department of Gynaecology, Paediatrics and Endocrinology (DFKE) > Clinic of Endocrinology, Diabetology and Clinical Nutrition

UniBE Contributor:

Schär, Ralph; Vajtai, Istvan and Sahli, Rahel Gerda

ISSN:

1752-1947

Publisher:

BioMed Central

Language:

English

Submitter:

Factscience Import

Date Deposited:

04 Oct 2013 14:18

Last Modified:

05 Feb 2017 01:34

Publisher DOI:

10.1186/1752-1947-5-496

PubMed ID:

21970745

BORIS DOI:

10.7892/boris.5576

URI:

https://boris.unibe.ch/id/eprint/5576 (FactScience: 210342)

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