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2024

Frauchiger, Bettina S; Willers, Corin; Cotting, Jasna; Kieninger, Elisabeth; Korten, Insa; Casaulta, Carmen; Salem, Yasmin; Stranzinger, Enno; Brabandt, Ben; Usemann, Jakob; Regamey, Nicolas; Kuhn, Alena; Blanchon, Sylvain; Rochat, Isabelle; Bauman, Grzegorz; Müller-Suter, Dominik; Moeller, Alexander; Latzin, Philipp; Ramsey, Kathryn A (2024). Lung structural and functional impairments in young children with cystic fibrosis diagnosed following newborn screening - A nationwide observational study. (In Press). Journal of cystic fibrosis Elsevier 10.1016/j.jcf.2024.05.010

Streibel, Carmen; Willers, C Corin; Bauman, Grzegorz; Pusterla, Orso; Bieri, Oliver; Curdy, Marion; Horn, Matthias; Casaulta, Carmen; Berger, Steffen; Dekany, Gabriela Marta; Kieninger, Elisabeth; Bartenstein, Andreas; Latzin, Philipp (2024). Long-term pulmonary outcome of children with congenital diaphragmatic hernia: functional lung MRI using matrix-pencil decomposition enables side-specific assessment of lung function. European radiology, 34(6), pp. 3773-3785. Springer-Verlag 10.1007/s00330-023-10395-8

Lam, Yin Ting; Papon, Jean-François; Alexandru, Mihaela; Anagiotos, Andreas; Armengot, Miguel; Boon, Mieke; Burgess, Andrea; Calmes, Doriane; Crowley, Suzanne; Dheyauldeen, Sinan Ahmed D; Emiralioglu, Nagehan; Erdem Eralp, Ela; van Gogh, Christine; Gokdemir, Yasemin; Haarman, Eric G; Harris, Amanda; Hayn, Isolde; Ismail-Koch, Hasnaa; Karadag, Bülent; Kempeneers, Céline; ... (2024). Association between upper and lower respiratory disease among patients with primary ciliary dyskinesia: an international study. ERJ Open Research, 10(2), 00932-2023. European Respiratory Society 10.1183/23120541.00932-2023

2023

Escher, Anaïs; Kieninger, Elisabeth; De Groof, Susan; Savas, Sibel T; Schneiter, Martin; Tschanz, Stefan A.; Frenz, Martin; Latzin, Philipp; Casaulta, Carmen; Müller, Loretta (2023). In Vitro Effect of Combined Hypertonic Saline and Salbutamol on Ciliary Beating Frequency and Mucociliary Transport in Human Nasal Epithelial Cells of Healthy Volunteers and Patients with Cystic Fibrosis. Journal of aerosol medicine and pulmonary drug delivery, 36(4), pp. 171-180. Mary Ann Liebert 10.1089/jamp.2022.0026

Streibel, Carmen; Willers, Christoph C; Pusterla, Orso; Bauman, Grzegorz; Stranzinger, Enno; Brabandt, Ben; Bieri, Oliver; Curdy, Marion; Bullo, Marina; Frauchiger, Bettina Sarah; Korten, Insa Christina Severine; Krüger, Linn; Casaulta, Carmen; Ratjen, Felix; Latzin, Philipp; Kieninger, Elisabeth (2023). Effects of elexacaftor/tezacaftor/ivacaftor therapy in children with cystic fibrosis - a comprehensive assessment using lung clearance index, spirometry, and functional and structural lung MRI. Journal of cystic fibrosis, 22(4), pp. 615-622. Elsevier 10.1016/j.jcf.2022.12.012

Frauchiger, Bettina S; Ramsey, Kathryn A; Usemann, Jakob; Kieninger, Elisabeth; Casaulta, Carmen; Sirtes, Daniel; Yammine, Sophie; Spycher, Ben; Moeller, Alexander; Latzin, Philipp (2023). Variability of clinically measured lung clearance index in children with cystic fibrosis. Pediatric pulmonology, 58(1), pp. 197-205. Wiley-Blackwell 10.1002/ppul.26180

2022

Kieninger, Elisabeth; Willers, Corin; Röthlisberger, Katrin; Yammine, Sophie; Pusterla, Orso; Bauman, Grzegorz; Stranzinger, Enno; Bieri, Oliver; Latzin, Philipp; Casaulta, Carmen (2022). Effect of Salbutamol on Lung Ventilation in Children with Cystic Fibrosis: Comprehensive Assessment Using Spirometry, Multiple-Breath Washout, and Functional Lung Magnetic Resonance Imaging. Respiration, 101(3), pp. 281-290. Karger 10.1159/000519751

Korten, Insa; Kieninger, Elisabeth; Krueger, Linn; Bullo, Marina; Flück, Christa E; Latzin, Philipp; Casaulta, Carmen; Boettcher, Claudia (2022). Short-Term Effects of Elexacaftor/Tezacaftor/Ivacaftor Combination on Glucose Tolerance in Young People With Cystic Fibrosis—An Observational Pilot Study. Frontiers in Pediatrics, 10 Frontiers 10.3389/fped.2022.852551

2021

Nussbaumer, Mirjam; Kieninger, Elisabeth; Tschanz, Stefan A.; Savas, Sibel T; Casaulta, Carmen; Goutaki, Myrofora; Blanchon, Sylvain; Jung, Andreas; Regamey, Nicolas; Kuehni, Claudia E.; Latzin, Philipp; Müller, Loretta Lina (2021). Diagnosis of primary ciliary dyskinesia: discrepancy according to different algorithms. ERJ Open Research, 7(4), 00353-2021. European Respiratory Society 10.1183/23120541.00353-2021

Müller, Loretta; Savas, Sibel T.; Tschanz, Stefan A.; Stokes, Andrea; Escher, Anaïs; Nussbaumer, Mirjam; Bullo, Marina; Kuehni, Claudia E.; Blanchon, Sylvain; Jung, Andreas; Regamey, Nicolas; Haenni, Beat; Schneiter, Martin; Ingold, Jonas; Kieninger, Elisabeth; Casaulta, Carmen; Latzin, Philipp (2021). A Comprehensive Approach for the Diagnosis of Primary Ciliary Dyskinesia—Experiences from the First 100 Patients of the PCD-UNIBE Diagnostic Center. Diagnostics, 11(9), p. 1540. MDPI 10.3390/diagnostics11091540

Bernasconi, Nadine; Kieninger, Elisabeth; Shaw, Michelle; Kurz, Johanna; Moeller, Alexander; Ratjen, Felix; Rochat, Isabelle; Stanojevic, Sanja; Singer, Florian (2021). CFTR-function and ventilation inhomogeneity in individuals with cystic fibrosis. Journal of cystic fibrosis, 20(4), pp. 641-647. Elsevier 10.1016/j.jcf.2020.12.009

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