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2024

Nilius, Henning; Hamzeh-Cognasse, Hind; Hastings, Janna; Studt, Jan-Dirk; Tsakiris, Dimitrios A; Greinacher, Andreas; Mendez, Adriana; Schmidt, Adrian Emanuel; Wuillemin, Walter A; Gerber, Bernhard; Vishnu, Prakash; Graf, Lukas; Kremer Hovinga, Johanna A; Bakchoul, Tamam; Cognasse, Fabrice; Nagler, Michael (2024). Proteomic profiling for biomarker discovery in heparin-induced thrombocytopenia. Blood advances, 8(11), pp. 2825-2834. American Society of Hematology 10.1182/bloodadvances.2024012782

Scully, Marie; Antun, Ana; Cataland, Spero R; Coppo, Paul; Dossier, Claire; Biebuyck, Nathalie; Hassenpflug, Wolf-Achim; Kentouche, Karim; Knöbl, Paul; Kremer Hovinga, Johanna A; López-Fernández, M Fernanda; Matsumoto, Masanori; Ortel, Thomas L; Windyga, Jerzy; Bhattacharya, Indranil; Cronin, Michael; Li, Hong; Mellgård, Björn; Patel, Munjal; Patwari, Parth; ... (2024). Recombinant ADAMTS13 in Congenital Thrombotic Thrombocytopenic Purpura. The New England journal of medicine, 390(17), pp. 1584-1596. Massachusetts Medical Society 10.1056/NEJMoa2314793

Schimmer, Roman R; Sutter, Tabea; Bachofner, Adrian; Ranieri, Elisabetta; Rodewald, Ann-Kathrin; Kremer Hovinga, Johanna A; Kimmich, Nina; Trinchero, Alice; Studt, Jan-Dirk (2024). Successful management of refractory immune-mediated thrombotic thrombocytopenic purpura during pregnancy and delivery using the anti-VWF nanobody caplacizumab. British journal of haematology, 204(5), pp. 1994-1998. Wiley-Blackwell 10.1111/bjh.19284

Scutelnic, Adrian; van de Munckhof, Anita; Miraclin, Angel T; Aaron, Sanjith; Hameed, Sajid; Wasay, Mohammad; Grosu, Oxana; Krzywicka, Katarzyna; Sánchez van Kammen, Mayte; Lindgren, Erik; Moreira, Tiago; Acampora, Roberto; Negro, Alberto; Karapanayiotides, Theodoros; Yaghi, Shadi; Revert, Anna; Cuadrado Godia, Elisa; Garcia-Madrona, Sebastian; La Spina, Paolino; Grillo, Francesco; ... (2024). Characteristics and outcomes of cerebral venous thrombosis associated with COVID-19. (In Press). European stroke journal, p. 23969873241241885. Sage 10.1177/23969873241241885

Larsen, Emil List; Nilius, Henning; Studt, Jan-Dirk; Tsakiris, Dimitrios A; Greinacher, Andreas; Mendez, Adriana; Schmidt, Adrian; Wuillemin, Walter A; Gerber, Bernhard; Vishnu, Prakash; Graf, Lukas; Kremer Hovinga, Johanna A; Goetze, Jens P; Bakchoul, Tamam; Nagler, Michael (2024). Accuracy of Diagnosing Heparin-Induced Thrombocytopenia. JAMA Network Open, 7(3) American Medical Association 10.1001/jamanetworkopen.2024.3786

Lämmle, Bernhard; Vanhoorelbeke, Karen; Kremer Hovinga, Johanna A.; Knöbl, Paul (2024). 100 Years of Thrombotic Thrombocytopenic Purpura: A Story of Death and Life. Hämostaseologie, 44(1), pp. 59-73. Thieme 10.1055/a-2223-9484

Castaman, Giancarlo; Peyvandi, Flora; Kremer Hovinga, Johanna A; Schutgens, Roger E G; Robson, Susan; Moreno, Katya; Jiménez-Yuste, Víctor (2024). Surgical Experience from the STASEY Study of Emicizumab Prophylaxis in People with Hemophilia A with Factor VIII Inhibitors. TH open, 8(1), e42-e54. Thieme 10.1055/s-0043-1777766

2023

Scutelnic, Adrian; van de Munckhof, Anita; Krzywicka, Katarzyna; van Kammen, Mayte Sánchez; Lindgren, Erik; Cordonnier, Charlotte; Kleinig, Timothy J; Field, Thalia S; Poli, Sven; Lemmens, Robin; Middeldorp, Saskia; Aaron, Sanjith; Borhani-Haghighi, Afshin; Arauz, Antonio; Kremer Hovinga, Johanna A; Günther, Albrecht; Putaala, Jukka; Wasay, Mohammad; Conforto, Adriana Bastos; de Sousa, Diana Aguiar; ... (2023). Sex differences in cerebral venous sinus thrombosis after adenoviral vaccination against COVID-19. European stroke journal, 8(4), pp. 1001-1010. Sage 10.1177/23969873231185213

Barton, J Cameron; Anderson, Cooper; Miranda, Frida Z; Kelley, Rachel; Kremer Hovinga, Johanna A; Terrell, Deirdra; Vesely, Sara K; George, James N; Muia, Joshua (2023). Cattle-FRETS71, a Novel Fluorogenic Substrate with Broad Applicability for Characterizing ADAMTS13 Properties and Function. Journal of thrombosis and haemostasis, 21(12), pp. 3393-3401. Wiley-Blackwell 10.1016/j.jtha.2023.08.016

Hammerer-Lercher, Angelika; Nilius, Henning; Studt, Jan-Dirk; Tsakiris, Dimitrios A; Greinacher, Andreas; Mendez, Adriana; Schmidt, Adrian; Wuillemin, Walter A; Gerber, Bernhard; Kremer Hovinga, Johanna A; Vishnu, Prakash; Graf, Lukas; Bakchoul, Tamam; Nagler, Michael (2023). Limited concordance of heparin/PF4 antibody assays for the diagnosis of heparin-induced thrombocytopenia: an analysis of the TORADI-HIT study. Journal of thrombosis and haemostasis, 21(9), pp. 2559-2568. Wiley-Blackwell 10.1016/j.jtha.2023.05.016

Miesbach, Wolfgang; Oldenburg, Johannes; Klamroth, Robert; Eichler, Hermann; Koscielny, Jürgen; Holzhauer, Susanne; Holstein, Katharina; Kremer Hovinga, Johanna A; Alberio, Lorenzo; Olivieri, Martin; Knöfler, Ralf; Male, Christoph; Tiede, Andreas (2023). Gentherapie der Hämophilie: Empfehlung der Gesellschaft für Thrombose- und Hämostaseforschung (GTH). Hämostaseologie, 43(3), pp. 196-207. Thieme 10.1055/a-1957-4477

Ruberti, Andrea Alberto; Kremer Hovinga, Johanna A; Federico, Nappi; Aurora, Vettese; Elena, Bianchi; Eliana, Fernandes; Elena, Galfetti; Rita, Monotti; Pamella, Paul; Stefano, Regazzoni; Daniela, Valente; Davide, Rossi; Georg, Stussi; Bernhard, Gerber (2023). Acquired haemophilia A in southern Switzerland from 2013 to 2019: a case series. Swiss medical weekly, 153, p. 40048. EMH Schweizerischer Ärzteverlag 10.57187/smw.2023.40048

Vrotniakaite-Bajerciene, Kristina; Tritschler, Tobias; Jalowiec, Katarzyna Aleksandra; Broughton, Helen; Schmidli, Fabienne; Schneider, Jenny Sarah; Haynes, Alan; Rovo, Alicia; Kremer Hovinga, Johanna Anna; Aujesky, Drahomir; Angelillo, Anne (2023). Adherence to thrombophilia testing guidelines and its influence on anticoagulation therapy: A single-center cross-sectional study. Thrombosis research, 223, pp. 87-94. Elsevier 10.1016/j.thromres.2022.12.001

Nilius, Henning; Cuker, Adam; Haug, Sigve; Nakas, Christos; Studt, Jan-Dirk; Tsakiris, Dimitrios A; Greinacher, Andreas; Mendez, Adriana; Schmidt, Adrian; Wuillemin, Walter A; Gerber, Bernhard; Kremer, Johanna A; Vishnu, Prakash; Graf, Lukas; Kashev, Alexander; Sznitman, Raphael; Bakchoul, Tamam; Nagler, Michael (2023). A machine-learning model for reducing misdiagnosis in heparin-induced thrombocytopenia: A prospective, multicenter, observational study. EClinicalMedicine, 55, p. 101745. Elsevier 10.1016/j.eclinm.2022.101745

2022

Asmis, Lars M; Serra, Andreas; Krafft, Alexander; Licht, Abraham; Leisinger, Elke; Henschkowski-Serra, Jana; Ganter, Michael T; Hauptmann, Steffen; Tinguely, Marianne; Kremer Hovinga, Johanna A (2022). Recombinant ADAMTS13 for Hereditary Thrombotic Thrombocytopenic Purpura. The New England journal of medicine, 387(25), pp. 2356-2361. Massachusetts Medical Society 10.1056/NEJMoa2211113

Scully, Marie; de la Rubia, Javier; Pavenski, Katerina; Metjian, Ara; Knöbl, Paul; Peyvandi, Flora; Cataland, Spero; Coppo, Paul; Kremer Hovinga, Johanna A; Minkue Mi Edou, Jessica; De Passos Sousa, Rui; Callewaert, Filip; Gunawardena, Sriya; Lin, Julie (2022). Long-term follow-up of patients treated with caplacizumab and safety and efficacy of repeat caplacizumab use: Post-HERCULES study. Journal of thrombosis and haemostasis, 20(12), pp. 2810-2822. Wiley-Blackwell 10.1111/jth.15892

Tarasco, Erika; Kremer Hovinga, Johanna; Schaller, Monica (1 October 2022). Thrombotic thrombocytopenic purpura - role of ADAMTS13 and long-term outcome.

Scutelnic, Adrian; Krzywicka, Katarzyna; Mbroh, Joshua; van de Munckhof, Anita; Sánchez van Kammen, Mayte; Aguiar de Sousa, Diana; Lindgren, Erik; Jood, Katarina; Günther, Albrecht; Hiltunen, Sini; Putaala, Jukka; Tiede, Andreas; Maier, Frank; Kern, Rolf; Bartsch, Thorsten; Althaus, Katharina; Ciccone, Alfonso; Wiedmann, Markus; Skjelland, Mona; Medina, Antonio; ... (2022). Management of cerebral venous thrombosis due to adenoviral COVID-19 vaccination. Annals of neurology, 92(4), pp. 562-573. Wiley-Blackwell 10.1002/ana.26431

van de Munckhof, Anita; Lindgren, Erik; Kleinig, Timothy J; Field, Thalia S; Cordonnier, Charlotte; Krzywicka, Katarzyna; Poli, Sven; Sánchez van Kammen, Mayte; Borhani-Haghighi, Afshin; Lemmens, Robin; Scutelnic, Adrian; Ciccone, Alfonso; Gattringer, Thomas; Wittstock, Matthias; Dizonno, Vanessa; Devroye, Annemie; Elkady, Ahmed; Günther, Albrecht; Cervera, Alvaro; Mengel, Annerose; ... (2022). Outcomes of Cerebral Venous Thrombosis due to Vaccine-Induced Immune Thrombotic Thrombocytopenia After the Acute Phase. Stroke, 53(10), pp. 3206-3210. Lippincott Williams & Wilkins 10.1161/STROKEAHA.122.039575

Tarasco, Erika; von Krogh, Anne Sophie; Hrdlickova, Radomira; Braschler, Thomas R; Iwaniec, Teresa; Knöbl, Paul N; Hamada, Eriko; Pikovsky, Oleg; Farese, Stefan; Gutwein, Odit; Kessler, Petr; Schultz, Nina H; von Auer, Charis; Windyga, Jerzy; Friedman, Kenneth; Hrachovinova, Ingrid; George, James N; Matsumoto, Masanori; Schneppenheim, Reinhard; Lämmle, Bernhard; ... (2022). Hereditary thrombotic thrombocytopenic purpura and COVID-19: Impacts of vaccination and infection in this rare disease. Research and practice in thrombosis and haemostasis, 6(7), e12814. Wiley 10.1002/rth2.12814

Draxler, Domink F; Brodard, Justine; Zante, Björn; Jakob, Stephan M; Wiegand, Jan; Kremer Hovinga, Johanna A; Angelillo-Scherrer, Anne; Rovo, Alicia (2022). The potential impact of Covid-19 on the capacity of routine laboratory tests to detect heparin-induced thrombocytopenia. Thrombosis journal, 20(1), p. 55. BioMed Central 10.1186/s12959-022-00411-0

Borogovac, Azra; Tarasco, Erika; Kremer Hovinga, Johanna A; Friedman, Kenneth D; Asch, Adam S; Vesely, Sara K; Prodan, Calin; Terrell, Deirdra R; George, James N (2022). Prevalence of Neuropsychiatric Symptoms and Stroke in Patients with Hereditary Thrombotic Thrombocytopenic Purpura. Blood, 140(7), pp. 785-789. American Society of Hematology 10.1182/blood.2022016044

Vrotniakaite-Bajerciene, Kristina; Tritschler, Tobias; Jalowiec, Katarzyna Aleksandra; Broughton, Helen; Brodard, Justine; Porret, Naomi; Haynes, Alan; Rovo, Alicia; Kremer Hovinga, Johanna Anna; Aujesky, Drahomir; Angelillo-Scherrer, Anne (2022). Thrombophilia Impact on Treatment Decisions, Subsequent Venous or Arterial Thrombosis and Pregnancy-Related Morbidity: A Retrospective Single-Center Cohort Study. Journal of clinical medicine, 11(14), p. 4188. MDPI 10.3390/jcm11144188

Heeb, Silvan R; Schaller Tschan, Monica Maria; Kremer Hovinga, Johanna A (2022). Naturally Occurring Anti-Idiotypic Antibodies Portray a Largely Private Repertoire in Immune-Mediated Thrombotic Thrombocytopenic Purpura. Journal of immunology, 208(11), pp. 2497-2507. American Association of Immunologists 10.4049/jimmunol.2100868

Buetler, Vanessa Alexandra; Agbariah, Nada; Schild, Deborah Pia; Liechti, Fabian D; Wieland, Anna; Andina, Nicola; Hammann, Felix; Kremer Hovinga, Johanna A (2022). Immune-Mediated Thrombotic Thrombocytopenic Purpura Following mRNA-Based COVID-19 Vaccine BNT162b2: Case Report and Mini-Review of the Literature. Frontiers in medicine, 9, p. 890661. Frontiers 10.3389/fmed.2022.890661

Krzywicka, Katarzyna; van de Munckhof, Anita; Zimmerman, Julian; Bode, Felix J; Frisullo, Giovanni; Karapanayiotides, Theodoros; Pötzsch, Bernd; Sanchez Van Kammen, Mayte; Heldner, Mirjam R.; Arnold, Marcel; Kremer Hovinga, Johanna Anna; Ferro, Jose M; Aguiar de Sousa, Diana; Coutinho, Jonathan M (2022). Cerebral venous thrombosis due to vaccine-induced immune thrombotic thrombocytopenia after a second ChAdOx1 nCoV-19 dose. Blood, 139(17), pp. 2720-2724. American Society of Hematology 10.1182/blood.2021015329

Liniger, Sophia; Dantonello, Tobias; Diepold, Miriam; Aebi, Christoph; Brodard, Justine; Kremer Hovinga, Johanna A.; Rössler, Jochen Karl; Kartal-Kaess, Mutlu (2022). Severe acquired purpura fulminans in a child. Archives of disease in childhood, 107(3), p. 300. BMJ Publishing Group 10.1136/archdischild-2021-322379

Krzywicka, Katarzyna; van de Munckhof, Anita; Sánchez van Kammen, Mayte; Heldner, Mirjam R; Jood, Katarina; Lindgren, Erik; Tatlisumak, Turgut; Putaala, Jukka; Kremer Hovinga, Johanna A; Middeldorp, Saskia; Levi, Marcel M; Cordonnier, Charlotte; Arnold, Marcel; Zwinderman, Aeilko H; Ferro, José M; Coutinho, Jonathan M; Aguiar de Sousa, Diana (2022). Age-Stratified Risk of Cerebral Venous Sinus Thrombosis After SARS-CoV-2 Vaccination. Neurology, 98(7), e759-e768. American Academy of Neurology 10.1212/WNL.0000000000013148

Van den Berg, Jana; Kremer Hovinga, Johanna A.; Pfleger, Claudia; Hegemann, Inga; Stehle, Gregor Thomas; Holbro, Andreas; Studt, Jan-Dirk (2022). Daratumumab for immune thrombotic thrombocytopenic purpura. Blood advances, 6(3), pp. 993-997. American Society of Hematology 10.1182/bloodadvances.2021005124

van de Munckhof, Anita; Krzywicka, Katarzyna; Aguiar de Sousa, Diana; Sánchez van Kammen, Mayte; Heldner, Mirjam R.; Jood, Katarina; Lindgren, Erik; Tatlisumak, Turgut; Putaala, Jukka; Kremer Hovinga, Johanna A.; Middeldorp, Saskia; Levi, Marcel; Arnold, Marcel; Ferro, José M; Coutinho, Jonathan M (2022). Declining mortality of cerebral venous sinus thrombosis with thrombocytopenia after SARS-CoV-2 vaccination. European journal of neurology, 29(1), pp. 339-344. Wiley 10.1111/ene.15113

Mertins, Tamara; Nilius, Henning; Boss, Robin; Knuchel, Matthias; Signorell, Andri; Huber, Carola A; Blozik, Eva; Kremer Hovinga, Johanna Anna; Bachmann, Lucas M; Nagler, Michael (2022). Secondary prevention of venous thromboembolism: Predictors and outcomes of guideline adherence in a long-term prospective cohort study. Frontiers in cardiovascular medicine, 9, p. 963528. Frontiers 10.3389/fcvm.2022.963528

Scutelnic, Adrian; Brodard, Justine; Kremer Hovinga, Johanna A; Arnold, Marcel; Heldner, Mirjam R (2022). Cerebral Venous Sinus Thrombosis Associated with Vaccine-Induced Thrombotic Thrombocytopenia—A Narrative Review. Clinical and translational neuroscience, 6(2), p. 11. MDPI 10.3390/ctn6020011

2021

Sánchez van Kammen, Mayte; Aguiar de Sousa, Diana; Poli, Sven; Cordonnier, Charlotte; Heldner, Mirjam R.; van de Munckhof, Anita; Krzywicka, Katarzyna; van Haaps, Thijs; Ciccone, Alfonso; Middeldorp, Saskia; Levi, Marcel M; Kremer Hovinga, Johanna A.; Silvis, Suzanne; Hiltunen, Sini; Mansour, Maryam; Arauz, Antonio; Barboza, Miguel A; Field, Thalia S; Tsivgoulis, Georgios; Nagel, Simon; ... (2021). Characteristics and Outcomes of Patients With Cerebral Venous Sinus Thrombosis in SARS-CoV-2 Vaccine-Induced Immune Thrombotic Thrombocytopenia. JAMA neurology, 78(11), pp. 1314-1323. American Medical Association 10.1001/jamaneurol.2021.3619

Krzywicka, Katarzyna; Heldner, Mirjam R.; Sánchez van Kammen, Mayte; van Haaps, Thijs; Hiltunen, Sini; Silvis, Suzanne M; Levi, Marcel; Kremer Hovinga, Johanna A.; Jood, Katarina; Lindgren, Erik; Tatlisumak, Turgut; Putaala, Jukka; Aguiar de Sousa, Diana; Middeldorp, Saskia; Arnold, Marcel; Coutinho, Jonathan M; Ferro, José M (2021). Post-SARS-CoV-2-vaccination Cerebral Venous Sinus Thrombosis: an analysis of cases notified to the European Medicines Agency. European journal of neurology, 28(11), pp. 3656-3662. Wiley 10.1111/ene.15029

Rössler, Jochen Karl; Baumgartner, Iris; Kremer Hovinga, Johanna A. (2021). EHA Endorsement of the Second International Guidelines for the Diagnosis and Management of Hereditary Hemorrhagic Telangiectasia. HemaSphere, 5(11), e647. Wolters Kluwer Health 10.1097/HS9.0000000000000647

Nilius, Henning; Mertins, Tamara; Boss, Robin; Knuchel, Matthias; Blozik, Eva; Kremer Hovinga, Johanna Anna; Eichinger, Sabine; Nagler, Michael (2021). Long-Term Survival After Venous Thromboembolism: A Prospective Cohort Study. Frontiers in cardiovascular medicine, 8(749342), p. 749342. Frontiers 10.3389/fcvm.2021.749342

Sánchez van Kammen, Mayte; Heldner, Mirjam R.; Brodard, Justine; Scutelnic, Adrian; Silvis, Suzanne; Schroeder, Verena; Kremer Hovinga, Johanna A.; Middeldorp, Saskia; Levi, Marcel; Hiltunen, Sini; Lindgren, Erik; Mansour, Maryam; Arauz, Antonio; Barboza, Miguel A.; Zuurbier, Susanna M.; Aguiar de Sousa, Diana; Ferro, Jose M.; Fischer, Urs; Field, Thalia S.; Jood, Katarina; ... (2021). Frequency of Thrombocytopenia and Platelet Factor 4/Heparin Antibodies in Patients With Cerebral Venous Sinus Thrombosis Prior to the COVID-19 Pandemic. JAMA : the journal of the American Medical Association, 326(4), pp. 332-338. American Medical Association 10.1001/jama.2021.9889

Balduini, Carlo; Freson, Kathleen; Greinacher, Andreas; Gresele, Paolo; Kühne, Thomas; Scully, Marie; Bakchoul, Tamam; Coppo, Paul; Dovc Drnovsek, Tadeja; Godeau, Bertrand; Gruel, Yves; Rao, A Koneti; Kremer Hovinga, Johanna A.; Makris, Michael; Matzdorff, Axel; Mumford, Andrew; Pecci, Alessandro; Raslova, Hana; Rivera, José; Roberts, Irene; ... (2021). The EHA Research Roadmap: Platelet Disorders. HemaSphere, 5(7), e601. Wolters Kluwer Health 10.1097/HS9.0000000000000601

Tarasco, Erika; Bütikofer, Lukas; Friedman, Kenneth D; George, James N; Hrachovinova, Ingrid V; Knöbl, Paul; Matsumoto, Masanori; von Krogh, Anne Sophie; Aebi-Huber, Isabella; Cermakova, Zuzana; Górska-Kosicka, Magdalena; Jalowiec, Katarzyna A; Largiadèr, Carlo R; Prohaszka, Zoltan; Sinkovits, György; Windyga, Jerzy; Lämmle, Bernhard; Kremer Hovinga, Johanna A (2021). Annual Incidence and Severity of Acute Episodes in Hereditary Thrombotic Thrombocytopenic Purpura. Blood, 137(25), pp. 3563-3575. American Society of Hematology 10.1182/blood.2020009801

Brodard, Justine; Kremer Hovinga, Johanna A.; Fontana, Pierre; Studt, Jan-Dirk; Gruel, Yves; Greinacher, Andreas (2021). COVID-19 patients often show high-titer non-platelet-activating anti-PF4/heparin IgG antibodies. Journal of thrombosis and haemostasis, 19(5), pp. 1294-1298. Wiley-Blackwell 10.1111/jth.15262

Peyvandi, Flora; Cataland, Spero; Scully, Marie; Coppo, Paul; Knoebl, Paul; Kremer Hovinga, Johanna A.; Metjian, Ara; de la Rubia, Javier; Pavenski, Katerina; Minkue Mi Edou, Jessica; De Winter, Hilde; Callewaert, Filip (2021). Caplacizumab prevents refractoriness and mortality in acquired thrombotic thrombocytopenic purpura: integrated analysis. Blood advances, 5(8), pp. 2137-2141. American Society of Hematology 10.1182/bloodadvances.2020001834

Cuker, Adam; Cataland, Spero R; Coppo, Paul; de la Rubia, Javier; Friedman, Kenneth D; George, James N; Knoebl, Paul N; Kremer Hovinga, Johanna A.; Lämmle, Bernhard; Matsumoto, Masanori; Pavenski, Katerina; Peyvandi, Flora; Sakai, Kazuya; Sarode, Ravi; Thomas, Mari R; Tomiyama, Yoshiaki; Veyradier, Agnès; Westwood, John-Paul; Scully, Marie (2021). Redefining outcomes in immune TTP: an international working group consensus report. Blood, 137(14), pp. 1855-1861. American Society of Hematology 10.1182/blood.2020009150

Esteves Pereira, Michael; Bocksrucker, Christoph; Kremer Hovinga, Johanna Anna; Mueller, Martin; Daskalakis, Michael; Mansouri Taleghani, Behrouz; Nagler, Michael (2021). Immunoadsorption for the Treatment of Acquired Hemophilia: New Observational Data, Systematic Review, and Meta-Analysis. Transfusion medicine reviews, 35(2), pp. 125-134. Elsevier 10.1016/j.tmrv.2021.01.001

De Gaudenzi, Martina; Kremer Hovinga, Johanna A.; Rössler, Jochen; Kaess, Michael; Kartal-Kaess, Mutlu (2021). Psychische Gesundheit bei chronischen Erkrankungen am Beispiel der Hämophilie. Paediatrica, 32(2), pp. 13-16. Schweizerische Gesellschaft für Pädiatrie SGP 10.35190/d2021.2.2

2020

Fontana, Pierre; Alberio, Lorenzo; Albisetti, Manuela; Angelillo, Anne; Asmis, Lars M; Casini, Alessandro; Gerber, Bernhard; Graf, Lukas; Hegemann, Inga; Korte, Wolfgang; Martinez, Maria; Studt, Jan-Dirk; Tsakiris, Dimitrios A; Wuillemin, Walter A; Kremer Hovinga, Johanna A. (2020). Management of bleeding events and invasive procedures in patients with haemophilia A without inhibitors treated with emicizumab. Swiss medical weekly, 150, w20422. EMH Schweizerischer Ärzteverlag 10.4414/smw.2020.20422

Li, Ang; Kremer Hovinga, Johanna A. (2020). Laboratory surveillance of immune-mediated thrombotic thrombocytopenic purpura. Hematology. American Society of Hematology education program, 2020(1), pp. 82-84. American Society of Hematology 10.1182/hematology.2020000164

Mackie, Ian; Mancini, Ilaria; Muia, Joshua; Kremer Hovinga, Johanna; Nair, Sukesh; Machin, Sam; Baker, Ross (2020). International Council for Standardization in Haematology (ICSH) recommendations for laboratory measurement of ADAMTS13. International journal of laboratory hematology, 42(6), pp. 685-696. Wiley 10.1111/ijlh.13295

Kremer Hovinga, Johanna A.; Braschler, Thomas R; Buchkremer, Florian; Farese, Stefan; Hengartner, Heinz; Lovey, Pierre-Yves; Largiadèr, Carlo R.; Mansouri Taleghani, Behrouz; Tarasco, Erika (2020). Insights from the Hereditary Thrombotic Thrombocytopenic Purpura Registry: Discussion of Key Findings Based on Individual Cases from Switzerland. Hämostaseologie, 40(S 01), S5-S14. Thieme 10.1055/a-1282-2264

Jalowiec, Katarzyna A.; Andres, Martin; Mansouri Taleghani, Behrouz; Musa, Albulena; Dickenmann, Martina; Angelillo-Scherrer, Anne; Rovó, Alicia; Kremer Hovinga, Johanna Anna (2020). Acquired hemophilia A and plasma cell neoplasms: a case report and review of the literature. Journal of medical case reports, 14(1), p. 206. BioMed Central 10.1186/s13256-020-02505-7

Barco, Stefano; Sollfrank, Stefanie; Trinchero, Alice; Adenaeuer, Anke; Abolghasemi, Hassan; Conti, Laura; Häuser, Friederike; Kremer Hovinga, Johanna A.; Lackner, Karl J; Loewecke, Felicia; Miloni, Erwin; Vazifeh Shiran, Nader; Tomao, Luigi; Wuillemin, Walter A; Zieger, Barbara; Lämmle, Bernhard; Rossmann, Heidi (2020). Severe plasma prekallikrein deficiency: Clinical characteristics, novel KLKB1 mutations, and estimated prevalence. Journal of thrombosis and haemostasis, 18(7), pp. 1598-1617. Wiley-Blackwell 10.1111/jth.14805

Alberio, Lorenzo A.; Angelillo-Scherrer, Anne; Asmis, Lars M.; Casini, Alessandro; Fontana, Pierre; Graf, Lukas; Hegemann, Inga; Kremer Hovinga, Johanna A.; Korte, Wolfgang; Lecompte, Thomas; Martinez, Martina; Nagler, Michael; Studt, Jan-Dirk; Tsakiris, Dimitrios A.; Wuillemin, Walter A. (2020). Recommendations on the use of anticoagulants for the treatment of patients with heparin-induced thrombocytopenia in Switzerland. Swiss medical weekly, 150(w20210), w20210. EMH Media 10.4414/smw.2020.20210

Casini, Alessandro; Alberio, Lorenzo; Angelillo-Scherrer, Anne; Fontana, Pierre; Gerber, Bernhard; Graf, Lukas; Hegemann, Inga; Korte, Wolfgang; Kremer Hovinga, Johanna A.; Lecompte, Thomas; Martinez, Maria; Nagler, Michael; Studt, Jan-Dirk; Tsakiris, Dimitrios; Wuillemin, Walter; Asmis, Lars (2020). Suggestions for thromboprophylaxis and laboratory monitoring for in-hospital patients with COVID-19 - a Swiss consensus statement by the Working Party Hemostasis. Swiss medical weekly, 150(w20247), w20247. EMH Media 10.4414/smw.2020.20247

Tarasco, E.; Aebi-Huber, I.; Kremer Hovinga, J. A. (2020). Die erbliche Form der thrombotisch thrombozytopenischen Purpura (TTP) – selten, aber bei Schwangerschaftskomplikationen zu bedenken! Vasomed - die Fachzeitschrift für Gefässerkrankungen, 32(3), pp. 90-91. Viavital-Verl.-GmbH

Tarasco, Erika; Aebi-Huber, Isabella; Kremer Hovinga, Johanna A. (2020). The Hereditary TTP Registry: who we are, what we do, why you should join us. Leading Opinions. Hämatologie & Onkologie(3), pp. 6-8. Universimed

Knoebl, Paul; Cataland, Spero; Peyvandi, Flora; Coppo, Paul; Scully, Marie; Kremer Hovinga, Johanna A.; Metjian, Ara; de la Rubia, Javier; Pavenski, Katerina; Minkue Mi Edou, Jessica; De Winter, Hilde; Callewaert, Filip (2020). Efficacy and safety of open-label caplacizumab in patients with exacerbations of acquired thrombotic thrombocytopenic purpura in the HERCULES study. Journal of thrombosis and haemostasis, 18(2), pp. 479-484. Wiley-Blackwell 10.1111/jth.14679

Kremer Hovinga, Johanna A.; George, James N. (2020). Hereditary Thrombotic Thrombocytopenic Purpura. Reply. The New England journal of medicine, 382(4), pp. 394-395. Massachusetts Medical Society 10.1056/NEJMc1915670

Borogovac, Azra; Tarasco, Erika; Kremer Hovinga, Johanna A.; George, James N. (2020). Hypertension in patients with hereditary thrombotic thrombocytopenic purpura. eJHaem, 1(1), pp. 342-343. Wiley 10.1002/jha2.29

2019

Orosz, Zsuzsanna Z; Bárdos, Helga; Shemirani, Amir H; Beke Debreceni, Ildikó; Lassila, Riitta; Riikonen, Antti S; Kremer Hovinga, Johanna A.; Seiler, Theo G.; van Dorland, Hendrika A.; Schroeder, Verena; Boda, Zoltán; Nemes, László; Früh Epstein, Beatrice; Nagy, Bence; Facskó, Andrea; Kappelmayer, János; Muszbek, László (2019). Cellular Factor XIII, a Transglutaminase in Human Corneal Keratocytes. International journal of molecular sciences, 20(23) Molecular Diversity Preservation International MDPI 10.3390/ijms20235963

Kremer Hovinga, Johanna A.; George, James N (2019). Hereditary Thrombotic Thrombocytopenic Purpura. The New England journal of medicine, 381(17), pp. 1653-1662. Massachusetts Medical Society 10.1056/NEJMra1813013

Robertz, Judith; Andres, Martin; Mansouri Taleghani, Behrouz; Koneth, Irene; Binet, Isabelle; Kremer Hovinga, Johanna A. (2019). Obinutuzumab in two patients suffering from immune-mediated thrombotic thrombocytopenic purpura intolerant to rituximab. American journal of hematology, 94(10), E259-E261. Wiley-Liss 10.1002/ajh.25583

Angelillo-Scherrer, Anne; Mansouri Taleghani, Behrouz; Förger, Frauke; Baerlocher, Gabriela M.; Pabst, Thomas; Pöllinger, Alexander; Banz, Yara; Geiser, Thomas; Kremer Hovinga, Johanna A.; Rovó, Alicia (2019). Immunoadsorption and autologous transplantation for life-threatening primary antiphospholipid syndrome. Blood advances, 3(17), pp. 2664-2667. American Society of Hematology 10.1182/bloodadvances.2019000465

Tiefenbacher, Stefan; Albisetti, Manuela; Baker, Peter; Kappert, Guenther; Kitchen, Steve; Kremer Hovinga, Johanna A.; Pouplard, Claire; Scholz, Ute; Ternisien, Catherine; Borgvall, Carin; Vicente, Tiago; Belyanskaya, Larisa; Walter, Olaf; Oldenburg, Johannes (2019). Estimation of Nuwiq® (simoctocog alfa) activity using one-stage and chromogenic assays-Results from an international comparative field study. Haemophilia, 25(4), pp. 708-717. Wiley 10.1111/hae.13763

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